PYGB

glycogen phosphorylase B

Summary

The protein encoded by this gene is a glycogen phosphorylase found predominantly in the brain. The encoded protein forms homodimers which can associate into homotetramers, the enzymatically active form of glycogen phosphorylase. The activity of this enzyme is positively regulated by AMP and negatively regulated by ATP, ADP, and glucose-6-phosphate. This enzyme catalyzes the rate-determining step in glycogen degradation. [provided by RefSeq, Jul 2008]

Known Variants77 total

rsidPosition (GRCh37)AllelesClassClinVar
rs55988180020:25,228,573G/A
rs37694841520:25,228,824C/Tuncertain significance
rs209287608520:25,228,830A/Cuncertain significance
rs20102328920:25,228,836A/Tuncertain significance
rs20015456420:25,228,902A/Cuncertain significance
rs76578234520:25,228,912A/Guncertain significance
rs36816622620:25,228,928C/Auncertain significance
rs126908218920:25,228,945G/Auncertain significance
rs14696613820:25,228,984C/Glikely benign
rs20177150920:25,228,988C/Guncertain significance
rs227347320:25,229,231C/A
rs481355520:25,237,145C/A
rs105053587220:25,239,874G/Auncertain significance
rs20065150220:25,239,909C/Tuncertain significance
rs76965570820:25,239,910G/Auncertain significance
rs228155820:25,240,189G/C
rs1169995320:25,241,345C/Gregulatory region variant
rs613855620:25,243,310C/A
rs611511820:25,246,734G/Aintron variant
rs77343952720:25,252,028T/Cuncertain significance
rs19989664320:25,252,036A/Guncertain significance
rs75397059020:25,252,048G/Tuncertain significance
rs19974096520:25,252,067A/Guncertain significance
rs3548146720:25,255,239C/Tbenign
rs251571034720:25,255,289A/Guncertain significance
rs20168984120:25,255,318G/Tuncertain significance
rs225404620:25,257,215G/Aintron variant
rs37709779520:25,257,322A/Guncertain significance
rs20003682820:25,257,329C/Guncertain significance
rs208831534120:25,257,367C/Tuncertain significance
rs37168330420:25,257,900G/Auncertain significance
rs14957833520:25,257,915C/Tuncertain significance
rs52853405820:25,259,085C/Tuncertain significance
rs75201546420:25,261,025G/Tuncertain significance
rs76760903220:25,261,038G/Auncertain significance
rs20181315320:25,261,588G/Auncertain significance
rs3507384920:25,261,590G/Abenign
rs77101054020:25,261,618C/Tuncertain significance
rs77662240320:25,261,619G/Auncertain significance
rs19965591120:25,261,645G/Auncertain significance
rs19966337920:25,261,660C/Tuncertain significance
rs77922221320:25,262,719A/Guncertain significance
rs226179020:25,262,789T/A
rs251571859520:25,263,840T/Cuncertain significance
rs13967296520:25,266,900G/Aintron variant
rs75300920:25,268,661C/Tintron variant
rs20199583420:25,269,105A/Cuncertain significance
rs225805320:25,271,033C/A
rs143815138920:25,271,121C/Tuncertain significance
rs77724204120:25,271,127G/Auncertain significance
rs19955320620:25,271,163C/Auncertain significance
rs75413503420:25,271,186C/Tuncertain significance
rs251572487520:25,271,212G/Tuncertain significance
rs37702574220:25,271,243T/Cuncertain significance
rs14305924720:25,273,049G/Alikely benign
rs20110969120:25,273,053G/Auncertain significance
rs77277044820:25,273,087C/Guncertain significance
rs76333295720:25,273,104G/Tuncertain significance
rs20180596120:25,273,119A/Guncertain significance
rs77037644520:25,273,158G/Auncertain significance
rs76076979820:25,273,185G/Auncertain significance
rs20119036320:25,273,191G/Auncertain significance
rs13960619720:25,273,245A/Guncertain significance
rs117249154320:25,274,813T/Cuncertain significance
rs20021374420:25,274,871C/Tuncertain significance
rs20092197020:25,274,937G/Abenign
rs251573199620:25,276,251T/Cuncertain significance
rs20155218220:25,276,272T/Guncertain significance
rs208853040520:25,276,302A/Guncertain significance
rs75593322520:25,277,027A/Guncertain significance
rs251573377420:25,277,051T/Cuncertain significance
rs143568860120:25,277,064C/Tuncertain significance
rs146434443720:25,277,073G/Auncertain significance
rs56247923620:25,277,111G/Auncertain significance
rs20156611720:25,277,139C/Guncertain significance
rs20000679220:25,277,151G/Auncertain significance
rs77433547820:25,277,153G/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.