SF3A3

splicing factor 3a subunit 3

Summary

This gene encodes subunit 3 of the splicing factor 3a protein complex. The splicing factor 3a heterotrimer includes subunits 1, 2 and 3 and is necessary for the in vitro conversion of 15S U2 snRNP into an active 17S particle that performs pre-mRNA splicing. Subunit 3 interacts with subunit 1 through its amino-terminus while the zinc finger domain of subunit 3 plays a role in its binding to the 15S U2 snRNP. This gene has a pseudogene on chromosome 20. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Mar 2016]

Known Variants18 total

rsidPosition (GRCh37)AllelesClassClinVar
rs39320271:38,423,055C/T
rs285855981:38,426,354G/C
rs25261752501:38,435,388T/Cuncertain significance
rs1472503011:38,437,673G/Aintron variant
rs14757463881:38,442,558C/Tuncertain significance
rs1827024071:38,444,394C/Guncertain significance
rs1391189751:38,445,183G/Tuncertain significance
rs9187643971:38,446,282C/Alikely benign
rs125690271:38,449,163C/G
rs112108661:38,449,565T/Cintron variant
rs12161952241:38,449,878T/Cuncertain significance
rs7560756891:38,449,893T/Cuncertain significance
rs3740958261:38,450,405C/Tuncertain significance
rs25262268611:38,450,451T/Guncertain significance
rs1393683951:38,453,330T/Cuncertain significance
rs25262365621:38,453,463T/Cuncertain significance
rs25262366391:38,453,480C/Guncertain significance
rs7747591701:38,455,251T/Cuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.