SF3B3

splicing factor 3b subunit 3

Summary

This gene encodes subunit 3 of the splicing factor 3b protein complex. Splicing factor 3b, together with splicing factor 3a and a 12S RNA unit, forms the U2 small nuclear ribonucleoproteins complex (U2 snRNP). The splicing factor 3b/3a complex binds pre-mRNA upstream of the intron's branch site in a sequence independent manner and may anchor the U2 snRNP to the pre-mRNA. Splicing factor 3b is also a component of the minor U12-type spliceosome. Subunit 3 has also been identified as a component of the STAGA (SPT3-TAF(II)31-GCN5L acetylase) transcription coactivator-HAT (histone acetyltransferase) complex, and the TFTC (TATA-binding-protein-free TAF(II)-containing complex). These complexes may function in chromatin modification, transcription, splicing, and DNA repair. [provided by RefSeq, Jul 2008]

Known Variants31 total

rsidPosition (GRCh37)AllelesClassClinVar
rs250758256016:70,563,061A/Guncertain significance
rs54732946216:70,565,043G/A
rs20028444216:70,566,392A/Guncertain significance
rs77295516716:70,566,422C/Tuncertain significance
rs250759305916:70,569,264A/Guncertain significance
rs89494740016:70,569,265T/Auncertain significance
rs55697834416:70,570,587G/T
rs75727574516:70,573,046G/Auncertain significance
rs250760303416:70,575,603G/Tuncertain significance
rs77855801016:70,582,330C/Tuncertain significance
rs37439075616:70,582,333C/Tuncertain significance
rs77734248316:70,582,340T/Cuncertain significance
rs94092262916:70,587,724T/C
rs19392111816:70,588,447G/Tuncertain significance
rs14203295216:70,590,160C/Guncertain significance
rs130377875216:70,590,894G/Auncertain significance
rs250762800116:70,594,491G/Cuncertain significance
rs250762965016:70,595,552G/Auncertain significance
rs76921654216:70,597,878C/Auncertain significance
rs74725126916:70,597,895C/Tuncertain significance
rs75375487516:70,597,912A/Cuncertain significance
rs250763415416:70,599,046C/Auncertain significance
rs77996912916:70,601,347C/Tuncertain significance
rs156742605916:70,602,189A/Guncertain significance
rs20066237416:70,602,280G/Auncertain significance
rs250763916516:70,602,355A/Guncertain significance
rs14692661516:70,602,955C/Tuncertain significance
rs76176068416:70,603,028A/Guncertain significance
rs11450933816:70,608,636T/A
rs7971455716:70,609,997A/C
rs56509388316:70,610,687A/C

Gene information from NCBI Gene. Variant classifications from ClinVar.