SMAD7

SMAD family member 7

Summary

The protein encoded by this gene is a nuclear protein that binds the E3 ubiquitin ligase SMURF2. Upon binding, this complex translocates to the cytoplasm, where it interacts with TGF-beta receptor type-1 (TGFBR1), leading to the degradation of both the encoded protein and TGFBR1. Expression of this gene is induced by TGFBR1. Variations in this gene are a cause of susceptibility to colorectal cancer type 3 (CRCS3). Several transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jun 2010]

Known Variants60 total

rsidPosition (GRCh37)AllelesClassClinVar
rs36979475718:46,447,737C/Tlikely benign
rs380992318:46,447,817G/Csynonymous variant
rs76265339518:46,447,857G/Auncertain significance
rs75317061618:46,447,909C/Tuncertain significance
rs14949264418:46,447,937G/Abenign
rs78086370418:46,447,961C/Tuncertain significance
rs132821935918:46,447,990C/Tuncertain significance
rs380992218:46,448,129G/Csynonymous variant
rs650787418:46,448,805T/A
rs650787518:46,448,819C/A
rs809804118:46,448,875A/T
rs808582418:46,449,111T/Cregulatory region variant
rs5892087818:46,449,565C/T
rs722963918:46,450,976A/Gintron variant
rs493956718:46,451,873G/Aintron variant
rs1187439218:46,453,156A/G
rs493982718:46,453,463T/Cintron variantrisk factor
rs1295371718:46,453,929C/Tintron variant
rs994651018:46,458,227A/Cintron variant
rs446414818:46,459,032T/Cregulatory region variant
rs233710718:46,459,323C/Tregulatory region variant
rs723844218:46,461,786T/A
rs7895089318:46,468,718C/Tregulatory region variant
rs77351100618:46,468,880G/Auncertain significance
rs207015278118:46,468,905G/Tuncertain significance
rs376448218:46,468,946A/Gbenign
rs994512618:46,469,962C/T
rs373624218:46,474,746T/Clikely benign
rs55144664918:46,474,796G/Tuncertain significance
rs14568633018:46,474,797G/Abenign
rs251221294018:46,476,313T/Cuncertain significance
rs251221308618:46,476,362G/Tuncertain significance
rs55356561018:46,476,364G/Tuncertain significance
rs251221309718:46,476,365C/Alikely benign
rs97567509118:46,476,382G/Alikely benign
rs127274276918:46,476,407C/Tuncertain significance
rs105680806018:46,476,514G/Auncertain significance
rs90822230218:46,476,533C/Tuncertain significance
rs93965775718:46,476,540G/Alikely benign
rs101262681818:46,476,541G/Auncertain significance
rs207024562918:46,476,544G/Auncertain significance
rs131867401118:46,476,551C/Tuncertain significance
rs53646521618:46,476,561T/Cbenign
rs251221382018:46,476,575G/Tuncertain significance
rs97549351218:46,476,584C/Auncertain significance
rs76321909918:46,476,609C/Tlikely benign
rs103523606518:46,476,611G/Alikely benign
rs77893560918:46,476,629C/Tuncertain significance
rs122716478518:46,476,632G/Clikely benign
rs251221411018:46,476,662T/Clikely benign
rs95517273418:46,476,671C/Tuncertain significance
rs14420402618:46,476,680C/Tlikely benign
rs122499380818:46,476,682C/Tuncertain significance
rs122191791718:46,476,692C/Tuncertain significance
rs75562629818:46,476,707C/Tuncertain significance
rs118001590318:46,476,708C/Glikely benign
rs251221424318:46,476,710C/Auncertain significance
rs251221426418:46,476,717C/Guncertain significance
rs127513831718:46,476,740G/Cuncertain significance
rs75248011118:46,476,761G/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.