SMG6

SMG6 nonsense mediated mRNA decay factor

Summary

This gene encodes a component of the telomerase ribonucleoprotein complex responsible for the replication and maintenance of chromosome ends. The encoded protein also plays a role in the nonsense-mediated mRNA decay (NMD) pathway, providing the endonuclease activity near the premature translation termination codon that is needed to initiate NMD. Alternatively spliced transcript variants encoding distinct protein isoforms have been described. [provided by RefSeq, Feb 2014]

Known Variants156 total

rsidPosition (GRCh37)AllelesClassClinVar
rs37182755117:1,964,805G/Auncertain significance
rs37652521417:1,964,815C/Guncertain significance
rs14122659917:1,964,826C/Tuncertain significance
rs14652302117:1,968,369T/Cuncertain significance
rs14099396617:1,968,376C/Tlikely benign
rs77844081417:1,968,769C/Tuncertain significance
rs119881616817:1,968,794C/Tuncertain significance
rs254362598617:1,968,848G/Auncertain significance
rs74658241917:1,968,886C/Tuncertain significance
rs20164159717:1,968,926G/Auncertain significance
rs76119189817:1,968,936C/Guncertain significance
rs76603629617:1,968,956C/Tuncertain significance
rs223248717:1,968,967T/Cuncertain significance
rs806823417:1,970,269G/Aregulatory region variant
rs213170417:1,970,898C/G
rs254365356317:1,972,119G/Auncertain significance
rs14481078417:1,972,183C/Tbenign
rs6174198017:1,972,221A/Guncertain significance
rs7619559817:1,974,511A/Tregulatory region variant
rs990167117:1,978,484T/Cintron variant
rs930324117:1,978,963T/Aregulatory region variant
rs479031117:1,979,188T/Cregulatory region variant
rs1295205117:1,982,790C/G
rs990825917:1,983,106C/Tintron variant
rs76825465717:1,985,128C/Auncertain significance
rs254374582417:1,985,175C/Guncertain significance
rs14116363917:1,985,204T/Cuncertain significance
rs5880195717:1,985,220C/Tbenign
rs76183387217:1,989,065A/Guncertain significance
rs479087317:1,994,966G/Tintron variant
rs990654617:1,995,614C/Gintron variant
rs406165917:1,997,444G/Cintron variant
rs11817005617:2,000,533C/Tintron variant
rs650324517:2,003,208G/Aintron variant
rs991511217:2,007,826A/Gdownstream gene variant
rs376023217:2,014,849G/Aintron variant
rs264143817:2,017,786C/Gintron variant
rs807253217:2,045,273G/T
rs806488517:2,047,564G/Aintron variant
rs650329317:2,048,611G/C
rs287319517:2,064,702A/C
rs479088117:2,068,932C/Aintron variant
rs5620929617:2,069,179A/Gregulatory region variant
rs122747119717:2,075,957C/Tuncertain significance
rs128611321817:2,076,040A/Guncertain significance
rs37098573817:2,076,064G/Auncertain significance
rs19161724917:2,076,084C/Guncertain significance
rs5713071217:2,089,035A/Gintron variant
rs722562317:2,089,548T/A
rs207199800317:2,089,991T/Auncertain significance
rs254439416817:2,090,045G/Auncertain significance
rs74962382817:2,090,062G/Auncertain significance
rs77531361317:2,090,074G/Auncertain significance
rs207200144717:2,090,087C/Tuncertain significance
rs14010025217:2,091,695T/Cuncertain significance
rs19969207417:2,091,788C/Tuncertain significance
rs13952871017:2,091,789G/Auncertain significance
rs100213517:2,097,583T/Gintron variant
rs1776172317:2,107,090C/Tdownstream gene variant
rs228172717:2,117,945A/C
rs123120617:2,125,605G/Aintron variant
rs21617217:2,126,504G/A
rs479088717:2,130,592C/T
rs991426617:2,133,250T/Cupstream gene variant
rs721722617:2,136,065T/Gintron variant
rs216935617:2,138,016A/C
rs55456936417:2,139,839A/Guncertain significance
rs36865014217:2,139,842C/Tuncertain significance
rs1085293217:2,143,460G/A
rs1107888417:2,145,193T/Cregulatory region variant
rs11225889417:2,157,817C/Tintron variant
rs5730723617:2,159,502A/Gintron variant
rs989122717:2,164,311G/Aintron variant
rs57618595617:2,167,393A/G
rs17004117:2,170,216C/Tregulatory region variant
rs7281957117:2,170,501G/C
rs1776186417:2,171,637C/T
rs18804370017:2,180,307T/Gintron variant
rs479032317:2,181,658A/T
rs148905363317:2,185,951C/Tuncertain significance
rs75701857917:2,186,011G/Auncertain significance
rs132268080617:2,186,018G/Cuncertain significance
rs19977664417:2,186,071C/Tuncertain significance
rs159778190517:2,186,128T/Cuncertain significance
rs93620349817:2,187,007T/Auncertain significance
rs21619117:2,188,639C/G
rs43220017:2,191,960A/Gintron variant
rs1294183617:2,194,874C/Gintron variant
rs77589911817:2,200,578T/Cuncertain significance
rs254485854517:2,200,624C/Guncertain significance
rs37411473817:2,200,631T/Cuncertain significance
rs21619917:2,200,871C/G
rs56529831717:2,201,177G/Tuncertain significance
rs78056056717:2,201,301C/Guncertain significance
rs74844479417:2,201,315G/Cuncertain significance
rs13896673817:2,201,323C/Tuncertain significance
rs21619717:2,201,944A/Gupstream gene variant
rs254486657117:2,202,211C/Auncertain significance
rs254486717717:2,202,290C/Guncertain significance
rs77938294317:2,202,291G/Auncertain significance

Showing 100 of 156 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.