SP3

Sp3 transcription factor

Summary

This gene belongs to a family of Sp1 related genes that encode transcription factors that regulate transcription by binding to consensus GC- and GT-box regulatory elements in target genes. This protein contains a zinc finger DNA-binding domain and several transactivation domains, and has been reported to function as a bifunctional transcription factor that either stimulates or represses the transcription of numerous genes. Transcript variants encoding different isoforms have been described for this gene, and one has been reported to initiate translation from a non-AUG (AUA) start codon. Additional isoforms, resulting from the use of alternate downstream translation initiation sites, have also been noted. A related pseudogene has been identified on chromosome 13. [provided by RefSeq, Feb 2010]

Known Variants42 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1858883922:174,774,677T/Cuncertain significance
rs13164746702:174,774,733A/Guncertain significance
rs7582980212:174,774,752C/Tlikely benign
rs5569881152:174,774,775C/Tuncertain significance
rs14532201142:174,774,789T/Guncertain significance
rs7759790322:174,774,827C/Auncertain significance
rs75615832:174,774,873T/Gbenign
rs24682203372:174,774,916A/Guncertain significance
rs5505461682:174,777,645T/C
rs16896713822:174,783,379C/Tuncertain significance
rs24682341612:174,783,381T/Cuncertain significance
rs789287382:174,783,428G/Abenign
rs7650249142:174,783,470C/Guncertain significance
rs576459082:174,801,862T/Aintron variant
rs5577333442:174,819,655T/Cuncertain significance
rs168419422:174,819,674T/Cbenign
rs24682861572:174,819,748C/Guncertain significance
rs14603822782:174,819,796T/Cuncertain significance
rs1467623152:174,819,979T/Cuncertain significance
rs3732623912:174,820,119T/Cuncertain significance
rs7572734732:174,820,146G/Auncertain significance
rs14226195312:174,820,175G/Cuncertain significance
rs7643540432:174,820,211T/Cuncertain significance
rs7516641792:174,820,215G/Cuncertain significance
rs14019558242:174,820,329T/Cuncertain significance
rs5737568692:174,820,360C/Tuncertain significance
rs7568152772:174,820,497C/Guncertain significance
rs7808110702:174,820,542T/Cuncertain significance
rs7615350902:174,820,609T/Guncertain significance
rs3743618772:174,820,635C/Tuncertain significance
rs12386769662:174,820,746A/Tuncertain significance
rs10476402:174,820,750C/Tbenign
rs7482647712:174,820,780C/Tuncertain significance
rs13970000562:174,820,827T/Guncertain significance
rs24682887142:174,820,894G/Cuncertain significance
rs5476168672:174,820,896G/Auncertain significance
rs13857614282:174,820,897T/Cuncertain significance
rs8916993432:174,820,924G/Auncertain significance
rs1999655572:174,820,926G/Cuncertain significance
rs16911653302:174,828,499G/Auncertain significance
rs7566793132:174,828,503C/Auncertain significance
rs7711675382:174,828,511C/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.