SRPX

sushi repeat containing protein X-linked

Summary

Predicted to be an extracellular matrix structural constituent. Predicted to be involved in phagolysosome assembly. Predicted to act upstream of or within several processes, including negative regulation of cell proliferation involved in contact inhibition; positive regulation of extrinsic apoptotic signaling pathway in absence of ligand; and response to endoplasmic reticulum stress. Located in collagen-containing extracellular matrix. [provided by Alliance of Genome Resources, Apr 2025]

Known Variants42 total

rsidPosition (GRCh37)AllelesClassClinVar
rs141892408X:38,009,102C/Alikely benign
rs996408217X:38,009,119A/Guncertain significance
rs35318931X:38,009,121G/Amissense variant
rs145370296X:38,013,726C/Tbenign
rs149411980X:38,013,743T/Guncertain significance
rs773402989X:38,013,747C/Guncertain significance
rs764257772X:38,013,760C/Auncertain significance
rs1938093953X:38,013,776G/Auncertain significance
rs1938094599X:38,013,797C/Auncertain significance
rs144518030X:38,013,811C/Auncertain significance
rs778546396X:38,013,815G/Auncertain significance
rs374467231X:38,013,836G/Tuncertain significance
rs774622598X:38,016,206A/Glikely benign
rs112900563X:38,017,972A/Gintron variant
rs750284952X:38,019,287G/Aconflicting classifications of pathogenicity
rs140816750X:38,019,329C/Auncertain significance
rs1190585618X:38,019,391G/Alikely benign
rs377733865X:38,019,394G/Tuncertain significance
rs2519656749X:38,019,404T/Auncertain significance
rs1245866412X:38,020,188C/Auncertain significance
rs201000269X:38,020,192C/Guncertain significance
rs766812159X:38,020,200C/Guncertain significance
rs752895004X:38,020,225C/Guncertain significance
rs756386867X:38,020,230C/Glikely pathogenic
rs374069621X:38,020,250G/Cuncertain significance
rs202189372X:38,020,285G/Cuncertain significance
rs1123773X:38,020,288G/Abenign
rs747875312X:38,024,032T/Auncertain significance
rs749663913X:38,024,139G/Auncertain significance
rs375318852X:38,031,152G/Auncertain significance
rs777506032X:38,031,185C/Tuncertain significance
rs201634519X:38,031,191G/Auncertain significance
rs139698955X:38,031,235C/Tuncertain significance
rs753463967X:38,031,293G/Auncertain significance
rs759401506X:38,033,422T/Cuncertain significance
rs149885497X:38,033,425C/Auncertain significance
rs1938528568X:38,033,457A/Guncertain significance
rs369046467X:38,033,526G/Tconflicting classifications of pathogenicity
rs188197194X:38,037,600A/Gbenign
rs201383079X:38,079,996A/Cuncertain significance
rs770581532X:38,080,002G/Cuncertain significance
rs1485230353X:38,080,037G/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.