SULF2

sulfatase 2

Summary

Heparan sulfate proteoglycans (HSPGs) act as coreceptors for numerous heparin-binding growth factors and cytokines and are involved in cell signaling. Heparan sulfate 6-O-endosulfatases, such as SULF2, selectively remove 6-O-sulfate groups from heparan sulfate. This activity modulates the effects of heparan sulfate by altering binding sites for signaling molecules (Dai et al., 2005 [PubMed 16192265]).[supplied by OMIM, Mar 2008]

Known Variants78 total

rsidPosition (GRCh37)AllelesClassClinVar
rs228127920:46,290,250T/Cdownstream gene variant
rs53381054420:46,290,537C/Tuncertain significance
rs55176386720:46,290,589C/Tuncertain significance
rs131968483920:46,290,599G/Tuncertain significance
rs160257889220:46,291,824T/Cuncertain significance
rs96400358320:46,291,837C/Tuncertain significance
rs14537179720:46,291,893T/Cuncertain significance
rs14915585320:46,291,906T/Guncertain significance
rs252017377920:46,291,935G/Tuncertain significance
rs77304192420:46,292,200T/Auncertain significance
rs75989483420:46,292,210C/Tlikely benign
rs76808455020:46,292,211G/Auncertain significance
rs117748123520:46,292,218G/Tuncertain significance
rs14565966020:46,292,361C/Tlikely benign
rs1004885320:46,292,910C/Tbenign
rs76390930720:46,292,915T/Auncertain significance
rs126517235020:46,292,926T/Clikely benign
rs125373276120:46,292,931T/Cuncertain significance
rs121328137120:46,293,944T/Cuncertain significance
rs37324362420:46,293,994C/Tuncertain significance
rs75523458320:46,294,603C/Tuncertain significance
rs56793843220:46,294,683T/Auncertain significance
rs7362469220:46,295,000T/Cbenign
rs76364488320:46,295,029C/Tuncertain significance
rs75359701820:46,295,030G/Alikely benign
rs78058330620:46,295,041C/Tuncertain significance
rs20080476720:46,295,158C/Tuncertain significance
rs75545337620:46,295,173C/Tuncertain significance
rs11549523120:46,295,174G/Abenign
rs37329844420:46,300,949G/Cuncertain significance
rs144409675520:46,300,956T/Cuncertain significance
rs20039648320:46,300,962C/Tuncertain significance
rs37409991520:46,300,963G/Auncertain significance
rs14978753020:46,301,026C/Tuncertain significance
rs57513997720:46,301,065C/Tlikely benign
rs252027706220:46,301,089A/Guncertain significance
rs134769093720:46,301,093A/Cuncertain significance
rs36820343220:46,301,094T/Cuncertain significance
rs120207092320:46,305,242C/Guncertain significance
rs76293787020:46,305,259C/Tlikely benign
rs14107685020:46,305,296C/Tuncertain significance
rs104664183120:46,305,847G/Auncertain significance
rs75232840720:46,305,861T/Auncertain significance
rs3410776920:46,306,828T/Acoding sequence variant
rs55598305120:46,307,438G/Auncertain significance
rs37349130420:46,311,769C/Tuncertain significance
rs77947810620:46,311,866G/Cuncertain significance
rs76936173820:46,311,878G/Cuncertain significance
rs77276600120:46,311,880C/Tuncertain significance
rs11517901020:46,313,190G/Abenign
rs14240159820:46,318,883C/Tuncertain significance
rs36879069320:46,318,897C/Tuncertain significance
rs75311762720:46,318,898G/Auncertain significance
rs13960315720:46,318,953C/Tuncertain significance
rs208814968020:46,318,961C/Tuncertain significance
rs18893467620:46,318,977C/Tuncertain significance
rs129628332420:46,318,978A/Guncertain significance
rs20077551020:46,319,014T/Cuncertain significance
rs6173061920:46,331,275G/Alikely benign
rs14354333420:46,331,280C/Tuncertain significance
rs56201738220:46,365,452C/Tuncertain significance
rs77483282020:46,365,477C/Tuncertain significance
rs75493380920:46,365,521G/Auncertain significance
rs252189109720:46,365,539G/Tuncertain significance
rs56452499320:46,365,561C/Tuncertain significance
rs99167306120:46,365,587C/Auncertain significance
rs132524181620:46,365,670C/Tuncertain significance
rs102947486820:46,385,980C/Tuncertain significance
rs77677237420:46,385,992C/Auncertain significance
rs76182625620:46,385,993G/Auncertain significance
rs76488591420:46,386,019C/Tuncertain significance
rs20000798620:46,386,028G/Auncertain significance
rs13893194520:46,386,040G/Auncertain significance
rs19248331920:46,386,089C/Tlikely benign
rs601867720:46,392,065A/Gintron variant
rs481068520:46,400,713T/A
rs11178313820:46,413,137A/Gintron variant
rs11330509120:46,413,163C/Tintron variant

Gene information from NCBI Gene. Variant classifications from ClinVar.