SUN2

Sad1 and UNC84 domain containing 2

Summary

SUN1 (MIM 607723) and SUN2 are inner nuclear membrane (INM) proteins that play a major role in nuclear-cytoplasmic connection by formation of a 'bridge' across the nuclear envelope, known as the LINC complex, via interaction with the conserved luminal KASH domain of nesprins (e.g., SYNE1; MIM 608441) located in the outer nuclear membrane (ONM). The LINC complex provides a direct connection between the nuclear lamina and the cytoskeleton, which contributes to nuclear positioning and cellular rigidity (summary by Haque et al., 2010 [PubMed 19933576]).[supplied by OMIM, Nov 2010]

Known Variants402 total

rsidPosition (GRCh37)AllelesClassClinVar
rs91784125222:39,132,275G/Tuncertain significance
rs251792223822:39,132,279G/Tuncertain significance
rs19984287622:39,132,281G/Alikely benign
rs209280400122:39,132,286C/Tuncertain significance
rs251792259522:39,132,304G/Auncertain significance
rs37744543422:39,132,312C/Guncertain significance
rs78109979522:39,132,322C/Guncertain significance
rs74807449722:39,132,323G/Alikely benign
rs53596477622:39,132,332C/Guncertain significance
rs13799672722:39,132,348C/Tuncertain significance
rs37029815022:39,132,349G/Auncertain significance
rs160321022822:39,132,352G/Alikely benign
rs251792316222:39,132,353C/Guncertain significance
rs14026134422:39,132,368C/Tlikely benign
rs15029217622:39,132,369G/Auncertain significance
rs37542047122:39,132,378G/Auncertain significance
rs75115958222:39,132,383G/Tlikely benign
rs55909645322:39,132,385C/Tuncertain significance
rs74850814422:39,132,401A/Glikely benign
rs13870222:39,132,601A/Tbenign
rs251794805022:39,134,159G/Clikely benign
rs78173447422:39,134,173C/Tuncertain significance
rs37238110622:39,134,174G/Auncertain significance
rs148628784822:39,134,179T/Cuncertain significance
rs53977547122:39,134,184G/Alikely benign
rs77161658322:39,134,186G/Auncertain significance
rs77510725722:39,134,190C/Tlikely benign
rs36782847522:39,134,201G/Tuncertain significance
rs209282387522:39,134,205G/Auncertain significance
rs54940484222:39,134,216C/Tuncertain significance
rs14614152222:39,134,217G/Abenign
rs75525960322:39,134,221G/Auncertain significance
rs128503628222:39,134,228T/Guncertain significance
rs78164419922:39,134,234G/Tuncertain significance
rs251794986622:39,134,246C/Tuncertain significance
rs74981339222:39,134,261C/Tuncertain significance
rs76831855422:39,134,283C/Tlikely benign
rs156929458522:39,134,585T/Clikely benign
rs121645016822:39,134,597T/Clikely benign
rs251795705922:39,134,599G/Auncertain significance
rs209282766122:39,134,618T/Auncertain significance
rs77949047622:39,134,619G/Alikely benign
rs11263768522:39,134,643G/Abenign
rs102102736322:39,134,645C/Tuncertain significance
rs209282804922:39,134,653A/Guncertain significance
rs76962767322:39,134,660C/Guncertain significance
rs77289160322:39,134,669C/Tuncertain significance
rs76293008922:39,134,670G/Alikely benign
rs56631217322:39,134,680C/Tuncertain significance
rs14101399722:39,134,681G/Alikely benign
rs75772082622:39,134,698C/Tuncertain significance
rs18271032422:39,134,699G/Auncertain significance
rs251795848122:39,134,701A/Guncertain significance
rs75449917122:39,134,708C/Tuncertain significance
rs78063516022:39,134,709G/Alikely benign
rs94997998122:39,134,713C/Guncertain significance
rs106268722:39,134,715C/Tbenign
rs138472383522:39,134,732C/Tuncertain significance
rs74912904122:39,134,742G/Alikely benign
rs77089269522:39,134,754A/Tuncertain significance
rs74900353222:39,134,861G/Tlikely benign
rs37466725522:39,134,871T/Alikely benign
rs144696735622:39,134,891C/Tuncertain significance
rs77569703422:39,134,892G/Auncertain significance
rs137045708922:39,134,911C/Auncertain significance
rs57019329222:39,134,917G/Abenign
rs53724181622:39,134,923G/Tlikely benign
rs75080061522:39,134,925C/Tuncertain significance
rs36939741522:39,134,941G/Alikely benign
rs76682987622:39,134,944C/Tlikely benign
rs75215058822:39,134,945G/Auncertain significance
rs86847470422:39,134,955C/Tuncertain significance
rs813862222:39,134,956G/Alikely benign
rs135228512422:39,134,966G/Cuncertain significance
rs137035993922:39,134,973G/Auncertain significance
rs131895545022:39,134,980G/Alikely benign
rs37114174922:39,134,985C/Tuncertain significance
rs15001454922:39,134,986G/Alikely benign
rs104538881722:39,135,001A/Glikely benign
rs125390749522:39,135,004A/Glikely benign
rs74702386822:39,135,011G/Alikely benign
rs37213405822:39,135,337G/Clikely benign
rs37376757222:39,135,342C/Tuncertain significance
rs36764511722:39,135,343G/Auncertain significance
rs209283483422:39,135,362C/Tuncertain significance
rs14066142222:39,135,363G/Alikely benign
rs75807616622:39,135,377C/Tuncertain significance
rs75487331022:39,135,383G/Auncertain significance
rs53976003822:39,135,397C/Tuncertain significance
rs209283514922:39,135,398G/Auncertain significance
rs77790977622:39,135,417G/Alikely benign
rs14914027922:39,135,419T/Cbenign
rs251797229622:39,135,425G/Auncertain significance
rs251797242622:39,135,431G/Cuncertain significance
rs145208897022:39,135,447C/Tuncertain significance
rs7747065022:39,135,699T/Cbenign
rs251797803722:39,135,743A/Guncertain significance
rs141786703922:39,135,752T/Cuncertain significance
rs14497527022:39,135,763C/Tlikely benign
rs56753201422:39,135,764G/Alikely benign

Showing 100 of 402 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.