TBC1D30

TBC1 domain family member 30

Summary

Enables GTPase activator activity and small GTPase binding activity. Involved in negative regulation of cilium assembly and positive regulation of GTPase activity. Located in several cellular components, including ciliary basal body; cytosol; and nuclear body. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants40 total

rsidPosition (GRCh37)AllelesClassClinVar
rs187417327912:65,218,729G/Auncertain significance
rs141963652812:65,224,218T/Cuncertain significance
rs15078144712:65,224,220C/Tmissense variant
rs187492257312:65,225,921G/Auncertain significance
rs18114872412:65,225,988C/Tlikely benign
rs117094521112:65,226,059A/Guncertain significance
rs129563162412:65,230,269G/Tuncertain significance
rs75351460512:65,230,303G/Auncertain significance
rs75691696012:65,230,307G/Auncertain significance
rs253969755412:65,230,369A/Guncertain significance
rs74699255312:65,230,425C/Guncertain significance
rs79701035112:65,232,484C/Tuncertain significance
rs77349922112:65,232,498A/Guncertain significance
rs75654884812:65,237,225T/Cuncertain significance
rs20070952312:65,241,749G/T
rs93987612:65,252,118A/Gintron variant
rs74788189812:65,258,509C/Auncertain significance
rs135889302112:65,258,559G/Cuncertain significance
rs7409969512:65,260,537T/Abenign
rs90871825912:65,260,605G/Auncertain significance
rs134141855612:65,260,660A/Cuncertain significance
rs122622051412:65,264,457G/Auncertain significance
rs54513222912:65,264,465C/Tuncertain significance
rs19244085612:65,264,526G/Auncertain significance
rs253978283812:65,268,816G/Auncertain significance
rs90418457312:65,268,933C/Tuncertain significance
rs187895009612:65,268,972C/Tuncertain significance
rs55351108312:65,268,991G/Auncertain significance
rs90982283912:65,269,008A/Cuncertain significance
rs93987512:65,269,047G/Abenign
rs76717558112:65,269,066A/Tuncertain significance
rs141058190512:65,269,125A/Glikely benign
rs99844934912:65,269,170A/Glikely benign
rs77011859212:65,269,311C/Tuncertain significance
rs253978515912:65,269,315G/Auncertain significance
rs93559039512:65,269,336C/Tlikely benign
rs11756841912:65,269,339C/Tuncertain significance
rs253978551812:65,269,375C/Tuncertain significance
rs92058310612:65,269,431C/Tuncertain significance
rs75179815712:65,269,438G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.