TGDS

TDP-glucose 4,6-dehydratase

Summary

The protein encoded by this gene is a member of the short-chain dehydrogenases/reductases (SDR) superfamily, and is thought to contain a nicotinamide adenine dinucleotide (NAD) binding domain. This large SDR family of enzymes is involved in the metabolism of a variety of compounds, including prostaglandins, retinoids, lipids, steroid hormones, and xenobiotics. Mutations in this gene have been associated with Catel-Manzke syndrome, which is characterized by Pierre Robin sequence, and radial deviation of the index finger due to the presence of an accessory bone between the index finger and its proximal phalanx. Pierre Robin sequence is defined by an undersized jaw, backwards displacement of the tongue base that causes an obstruction of the airways, and can also be associated with a cleft palate. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2015]

Known Variants84 total

rsidPosition (GRCh37)AllelesClassClinVar
rs76167172813:95,227,039T/Clikely benign
rs53341710513:95,227,043G/Abenign
rs213950976313:95,227,050G/Auncertain significance
rs213950977213:95,227,055A/Guncertain significance
rs250194849013:95,227,075C/Glikely pathogenic
rs159443485413:95,227,093T/Clikely benign
rs144752008613:95,227,114G/Alikely benign
rs374210713:95,227,340C/Tbenign
rs14122284513:95,228,593A/Glikely benign
rs188859801013:95,228,606C/Auncertain significance
rs72416000513:95,228,658T/Cmissense variantpathogenic
rs77525396413:95,228,667T/Guncertain significance
rs250195690613:95,229,625C/Tuncertain significance
rs54623713613:95,229,675C/Guncertain significance
rs11640356813:95,229,697A/Gbenign
rs7354662313:95,229,735A/Gbenign
rs37377298213:95,230,239C/Alikely benign
rs75725433313:95,230,255A/Tuncertain significance
rs250195947013:95,230,291C/Tuncertain significance
rs250195976113:95,230,343T/Clikely benign
rs14378087213:95,230,370A/Clikely benign
rs54443673413:95,230,384A/Gmissense variantpathogenic
rs76641384413:95,230,399T/Guncertain significance
rs1694994013:95,230,877G/Abenign
rs74670483913:95,230,970T/Clikely benign
rs37533516113:95,230,976T/Clikely benign
rs142349289413:95,231,001T/Clikely benign
rs956163613:95,231,235C/Tbenign
rs227564813:95,231,981T/Cbenign
rs128536801513:95,232,167G/Auncertain significance
rs213951901013:95,232,181A/Cuncertain significance
rs250196882213:95,233,331C/Tlikely benign
rs20064328213:95,233,336A/Glikely benign
rs137667818113:95,233,346T/Guncertain significance
rs37048453313:95,233,353G/Cuncertain significance
rs213952170513:95,233,400G/Tuncertain significance
rs250196925513:95,233,409T/Guncertain significance
rs77286805713:95,233,419G/Cuncertain significance
rs188877925513:95,233,445T/Clikely pathogenic
rs955640213:95,233,607G/Abenign
rs477380113:95,235,175T/Cbenign
rs250197475613:95,235,329A/Glikely benign
rs77185679113:95,235,339T/Glikely benign
rs250197498613:95,235,365C/Auncertain significance
rs75908768513:95,235,399C/Tlikely benign
rs76489011313:95,235,415T/Cuncertain significance
rs18983814813:95,235,457T/Cuncertain significance
rs15027174613:95,235,477T/Clikely benign
rs11542367113:95,235,557A/Gbenign
rs11240168213:95,235,626A/Tbenign
rs448987313:95,242,527T/C
rs188917273813:95,243,106C/Tlikely pathogenic
rs14713924013:95,243,112T/Auncertain significance
rs77527383813:95,243,115G/Alikely pathogenic
rs14043095213:95,243,122C/Tmissense variantpathogenic
rs6174168513:95,243,123G/Abenign
rs72750280813:95,243,126A/Cmissense variantpathogenic
rs75421451013:95,243,134G/Tuncertain significance
rs75995237613:95,243,135T/Clikely benign
rs72416000413:95,243,151T/Cmissense variantpathogenic
rs159445594713:95,243,156T/Clikely benign
rs250199718713:95,243,205A/Tlikely benign
rs930197913:95,243,270G/Abenign
rs20194219013:95,244,490C/Tbenign
rs76440145713:95,244,537A/Tuncertain significance
rs213954451713:95,244,548T/Auncertain significance
rs37771716213:95,244,583G/Clikely benign
rs77335020713:95,246,112T/Guncertain significance
rs76072038013:95,246,122T/Clikely benign
rs125018703713:95,246,145C/Tuncertain significance
rs14447826813:95,246,151T/Clikely benign
rs142043278413:95,246,165T/Clikely benign
rs111237013:95,246,440T/Cbenign
rs11392515713:95,248,289C/Tbenign
rs125750968513:95,248,302T/Guncertain significance
rs3499113213:95,248,348C/Tbenign
rs93700378213:95,248,351C/Guncertain significance
rs77100238213:95,248,354G/Auncertain significance
rs74574871213:95,248,361C/Guncertain significance
rs20209767313:95,248,366G/Auncertain significance
rs18643856913:95,248,379C/Tbenign
rs36849909913:95,248,400C/Tlikely benign
rs229805813:95,248,566C/Tbenign
rs7890581913:95,248,751C/Tbenign

Gene information from NCBI Gene. Variant classifications from ClinVar.