TPM1

tropomyosin 1

Summary

This gene is a member of the tropomyosin family of highly conserved, widely distributed actin-binding proteins involved in the contractile system of striated and smooth muscles and the cytoskeleton of non-muscle cells. Tropomyosin is composed of two alpha-helical chains arranged as a coiled-coil. It is polymerized end to end along the two grooves of actin filaments and provides stability to the filaments. The encoded protein is one type of alpha helical chain that forms the predominant tropomyosin of striated muscle, where it also functions in association with the troponin complex to regulate the calcium-dependent interaction of actin and myosin during muscle contraction. In smooth muscle and non-muscle cells, alternatively spliced transcript variants encoding a range of isoforms have been described. Mutations in this gene are associated with type 3 familial hypertrophic cardiomyopathy and dilated cardiomyopathy 1Y. [provided by RefSeq, Jun 2022]

Known Variants724 total

rsidPosition (GRCh37)AllelesClassClinVar
rs380956615:63,333,724A/Gupstream gene variant
rs5596273615:63,333,892G/C
rs380956715:63,334,520C/Abenign
rs380956815:63,334,609C/Gbenign
rs382597315:63,334,635C/Gbenign
rs3582989715:63,334,688G/Cbenign
rs804283415:63,334,698C/Gbenign
rs87936466415:63,334,757A/Clikely benign
rs52858917315:63,334,765G/Alikely benign
rs56530190715:63,334,790C/Tlikely benign
rs1752584815:63,334,823G/Alikely benign
rs214059019615:63,334,840A/Gbenign
rs54104645015:63,334,843G/Aconflicting classifications of pathogenicity
rs103235791715:63,334,844G/Cconflicting classifications of pathogenicity
rs214059060115:63,334,877T/Gbenign
rs95704505215:63,334,904C/Gbenign
rs88605131915:63,334,915G/Auncertain significance
rs88605132015:63,334,923C/Tuncertain significance
rs53041057915:63,334,935G/Cuncertain significance
rs93056942515:63,334,956C/Tbenign
rs74752372015:63,334,981C/Tuncertain significance
rs37276031615:63,334,982G/Tuncertain significance
rs133594893215:63,334,988C/Tlikely benign
rs254241137415:63,335,014C/Guncertain significance
rs214059356015:63,335,015T/Cbenign
rs125768740415:63,335,016C/Auncertain significance
rs203141808715:63,335,017G/Auncertain significance
rs103484816615:63,335,019C/Tuncertain significance
rs37087130715:63,335,022C/Auncertain significance
rs254241153015:63,335,024C/Tuncertain significance
rs36754366815:63,335,029A/Guncertain significance
rs147563556415:63,335,030T/Cuncertain significance
rs106050186515:63,335,032G/Cuncertain significance
rs135093594315:63,335,034C/Tconflicting classifications of pathogenicity
rs254241167615:63,335,035G/Tuncertain significance
rs254241168815:63,335,036C/Tuncertain significance
rs254241170215:63,335,037C/Tlikely benign
rs73088114815:63,335,038A/Guncertain significance
rs214059411915:63,335,043G/Alikely benign
rs90050480015:63,335,045A/Guncertain significance
rs214059426615:63,335,049G/Alikely benign
rs254241184115:63,335,050A/Guncertain significance
rs39751636415:63,335,051T/Amissense variantuncertain significance
rs73088114915:63,335,053C/Auncertain significance
rs155540293115:63,335,054A/Tuncertain significance
rs39751636515:63,335,055G/Aconflicting classifications of pathogenicity
rs86830091315:63,335,058G/Auncertain significance
rs76688375815:63,335,059C/Tlikely benign
rs254241204515:63,335,061G/Clikely benign
rs203142601515:63,335,062A/Tuncertain significance
rs131354980115:63,335,064G/Alikely benign
rs143908026015:63,335,067C/Glikely benign
rs87666121015:63,335,068G/Tconflicting classifications of pathogenicity
rs254241213515:63,335,071A/Guncertain significance
rs86902553915:63,335,072A/Guncertain significance
rs19947630115:63,335,073G/Tconflicting classifications of pathogenicity
rs72750429015:63,335,074G/Cmissense variantpathogenic
rs75558136915:63,335,076G/Alikely benign
rs254241224115:63,335,077A/Cuncertain significance
rs87885415015:63,335,079C/Guncertain significance
rs254241226015:63,335,080G/Aconflicting classifications of pathogenicity
rs73088115015:63,335,081C/Auncertain significance
rs254241231415:63,335,085G/Tuncertain significance
rs72750439115:63,335,086G/Auncertain significance
rs143769847115:63,335,089C/Alikely benign
rs73088115115:63,335,090G/Tmissense variantpathogenic
rs39751638215:63,335,092G/Amissense variantpathogenic
rs203143197315:63,335,093C/Guncertain significance
rs19947630215:63,335,095G/Cuncertain significance
rs214059547015:63,335,096A/Cuncertain significance
rs87666139615:63,335,097G/Cuncertain significance
rs203143349215:63,335,098C/Tuncertain significance
rs203143381515:63,335,102C/Tuncertain significance
rs121419157615:63,335,103G/Alikely benign
rs214059565615:63,335,104G/Auncertain significance
rs73088023415:63,335,105A/Guncertain significance
rs77798111415:63,335,106G/Alikely benign
rs254241267615:63,335,107G/Auncertain significance
rs39751639115:63,335,110G/Auncertain significance
rs254241276115:63,335,111A/Cuncertain significance
rs125507166015:63,335,113A/Cuncertain significance
rs53023430115:63,335,115G/Alikely benign
rs254241287215:63,335,116A/Guncertain significance
rs39751639615:63,335,119G/Auncertain significance
rs77066191615:63,335,121G/Clikely benign
rs214059632115:63,335,122G/Tuncertain significance
rs254241302015:63,335,123C/Tuncertain significance
rs39751639715:63,335,125G/Auncertain significance
rs88603944415:63,335,126A/Cmissense variantuncertain significance
rs214059646815:63,335,127A/Glikely benign
rs254241310515:63,335,128G/Auncertain significance
rs159629734715:63,335,131A/Guncertain significance
rs73088115215:63,335,132G/Cuncertain significance
rs144873806115:63,335,133G/Cuncertain significance
rs156693623715:63,335,134A/Guncertain significance
rs117419498315:63,335,135G/Auncertain significance
rs254241323815:63,335,136C/Guncertain significance
rs19947630315:63,335,137A/Guncertain significance
rs214059674315:63,335,139G/Alikely benign
rs106050186315:63,335,140C/Guncertain significance

Showing 100 of 724 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.