URB1

URB1 ribosome biogenesis factor

Summary

Enables RNA binding activity. Predicted to be involved in maturation of 5.8S rRNA from tricistronic rRNA transcript (SSU-rRNA, 5.8S rRNA, LSU-rRNA) and maturation of LSU-rRNA from tricistronic rRNA transcript (SSU-rRNA, 5.8S rRNA, LSU-rRNA). Located in fibrillar center. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants173 total

rsidPosition (GRCh37)AllelesClassClinVar
rs19036462121:33,682,907C/Tdownstream gene variant
rs139769071221:33,687,297G/Auncertain significance
rs57139377821:33,687,330C/Tlikely benign
rs103162777821:33,687,331G/Cuncertain significance
rs76011663721:33,687,344G/Auncertain significance
rs56487639721:33,687,393C/Tuncertain significance
rs251689198321:33,688,806G/Auncertain significance
rs75076003921:33,688,854C/Tlikely benign
rs37768642521:33,688,948G/Auncertain significance
rs74914761421:33,688,953T/Cuncertain significance
rs37212073721:33,688,978C/Tuncertain significance
rs123892399921:33,689,086C/Auncertain significance
rs18996618521:33,689,149C/Tlikely benign
rs13949277521:33,689,156G/Alikely benign
rs54756803421:33,689,170C/Auncertain significance
rs36918597821:33,689,188G/Tuncertain significance
rs76222521:33,689,199G/Cbenign
rs251689250921:33,689,200G/Auncertain significance
rs37720107521:33,689,301C/Tuncertain significance
rs143618362621:33,689,337C/Tuncertain significance
rs183701680321:33,689,344G/Cuncertain significance
rs76812325721:33,689,999G/Auncertain significance
rs98401456521:33,690,016A/Guncertain significance
rs55340636921:33,690,017T/Cuncertain significance
rs37012032221:33,690,022G/Auncertain significance
rs203270924221:33,690,028A/Guncertain significance
rs37734059221:33,690,129G/Alikely benign
rs76777372921:33,690,176C/Tuncertain significance
rs145994001321:33,690,191C/Tuncertain significance
rs18304572021:33,691,527C/Tbenign
rs37451440521:33,691,569T/Cuncertain significance
rs36801200321:33,691,577G/Cuncertain significance
rs76473857121:33,691,591G/Auncertain significance
rs128794185321:33,691,626C/Tlikely benign
rs75127018121:33,691,664G/Clikely benign
rs145834476021:33,691,692A/Tuncertain significance
rs251689623221:33,694,124T/Cuncertain significance
rs98606342121:33,694,173G/Auncertain significance
rs77373614221:33,694,175C/Tuncertain significance
rs203277100821:33,694,178G/Cuncertain significance
rs77444482621:33,694,217C/Tuncertain significance
rs91941053921:33,694,218G/Cuncertain significance
rs95096317321:33,694,812C/Auncertain significance
rs203277972621:33,694,825G/Cuncertain significance
rs148606358221:33,694,828A/Guncertain significance
rs99632792321:33,696,887C/Tuncertain significance
rs94712627521:33,697,579T/Cuncertain significance
rs36781279121:33,697,668A/Tuncertain significance
rs77945406921:33,697,676A/Guncertain significance
rs104135988121:33,697,681C/Tuncertain significance
rs160112743021:33,705,689C/Auncertain significance
rs78013675521:33,706,474C/Tuncertain significance
rs56656861821:33,706,477G/Tuncertain significance
rs36885298421:33,706,527C/Tuncertain significance
rs74927171521:33,706,533C/Tuncertain significance
rs77022562721:33,706,546G/Alikely benign
rs14378176221:33,706,596C/Guncertain significance
rs251690462121:33,706,599C/Auncertain significance
rs7977146821:33,706,601C/Tbenign
rs76327336221:33,706,610A/Tuncertain significance
rs37252462421:33,709,442C/Tuncertain significance
rs203296888121:33,709,458T/Auncertain significance
rs20192146821:33,709,719C/Tuncertain significance
rs147055316621:33,709,732G/Alikely benign
rs77851624321:33,709,743C/Tuncertain significance
rs127724659121:33,709,767T/Cuncertain significance
rs37738613121:33,709,781G/Cuncertain significance
rs203297464321:33,709,790T/Auncertain significance
rs11664201921:33,711,053C/Tbenign
rs5813064521:33,711,077C/Tbenign
rs90115447821:33,711,086C/Tuncertain significance
rs37287248021:33,711,097C/Tlikely benign
rs136133274321:33,711,108G/Auncertain significance
rs14155061221:33,711,126G/Alikely benign
rs144113870121:33,711,133C/Tuncertain significance
rs124407022921:33,711,135G/Cuncertain significance
rs76609134821:33,711,166C/Tuncertain significance
rs105170438021:33,713,776T/Cuncertain significance
rs251691303721:33,717,027C/Tuncertain significance
rs102409564021:33,717,058C/Tuncertain significance
rs37416069621:33,717,722C/Tlikely benign
rs127776154921:33,717,746T/Cuncertain significance
rs96387408621:33,717,761G/Auncertain significance
rs37368646621:33,717,762G/Cuncertain significance
rs140666501221:33,717,870T/Guncertain significance
rs117033767021:33,719,307G/Auncertain significance
rs203309423921:33,719,345C/Tlikely benign
rs125689786421:33,719,346C/Guncertain significance
rs77601730321:33,719,419G/Alikely benign
rs89147100321:33,719,460G/Auncertain significance
rs20034308021:33,719,643T/Guncertain significance
rs135381557921:33,719,648G/Cuncertain significance
rs251691539021:33,719,692T/Auncertain significance
rs55179926621:33,719,700C/Tuncertain significance
rs11546530321:33,719,701G/Abenign
rs76214652121:33,719,739C/Guncertain significance
rs86867369121:33,719,828G/Alikely benign
rs75182611321:33,719,829G/Auncertain significance
rs86628667521:33,719,852G/Auncertain significance
rs77369483221:33,719,882A/Tuncertain significance

Showing 100 of 173 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.