USP39

ubiquitin specific peptidase 39

Summary

Predicted to enable cysteine-type deubiquitinase activity and zinc ion binding activity. Involved in spliceosomal complex assembly. Located in nucleoplasm. Part of U4/U6 x U5 tri-snRNP complex. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants39 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1434521532:85,832,897G/Cregulatory region variant
rs1924371302:85,840,200C/Tupstream gene variant
rs7530215362:85,843,325G/Alikely benign
rs7817413662:85,843,341A/Guncertain significance
rs7557063762:85,843,349G/Auncertain significance
rs7793692982:85,843,358C/Tuncertain significance
rs10445296152:85,843,392C/Tuncertain significance
rs11653109632:85,843,437C/Tuncertain significance
rs13906766632:85,843,442A/Cuncertain significance
rs9689521972:85,843,452G/Auncertain significance
rs7545523962:85,843,475G/Cuncertain significance
rs7467340292:85,843,491G/Tuncertain significance
rs3700057842:85,843,544C/Tuncertain significance
rs7810760692:85,843,550G/Auncertain significance
rs5737084602:85,845,951G/A
rs7500662932:85,846,374G/Clikely benign
rs16742656952:85,846,381C/Tuncertain significance
rs24664615032:85,848,701A/Tuncertain significance
rs7621470722:85,857,908A/Guncertain significance
rs1435391172:85,858,064A/Guncertain significance
rs65476292:85,860,228A/G
rs5466441682:85,863,120A/C
rs9985760922:85,863,219C/Guncertain significance
rs2006226712:85,863,239A/Guncertain significance
rs24665569552:85,864,492C/Guncertain significance
rs1914677122:85,865,754C/Tintron variant
rs1929571292:85,867,558C/Tintron variant
rs13293525842:85,868,140G/Cuncertain significance
rs14504798372:85,868,195A/Tuncertain significance
rs753794702:85,869,116A/Gintron variant
rs7787735312:85,872,075G/Auncertain significance
rs3746406242:85,872,133A/Guncertain significance
rs7632977122:85,872,174G/Cuncertain significance
rs728466292:85,873,907G/Aintron variant
rs585888202:85,874,044C/A
rs24666154542:85,875,092A/Guncertain significance
rs16768375192:85,875,903A/Guncertain significance
rs3756272722:85,875,914A/Guncertain significance
rs3715817542:85,875,923G/Cuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.