USP4

ubiquitin specific peptidase 4

Summary

The protein encoded by this gene is a protease that deubiquitinates target proteins such as ADORA2A and TRIM21. The encoded protein shuttles between the nucleus and cytoplasm and is involved in maintaining operational fidelity in the endoplasmic reticulum. Three transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Oct 2011]

Known Variants62 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1477015613:49,315,843A/Cuncertain significance
rs13138311763:49,315,859T/Cuncertain significance
rs7783276903:49,316,276C/Tuncertain significance
rs7757727573:49,318,194G/Tuncertain significance
rs12063276113:49,318,219T/Cuncertain significance
rs15755984953:49,318,256G/Alikely benign
rs412907003:49,321,424T/Cbenign
rs1428350153:49,321,436C/Tuncertain significance
rs1398283273:49,321,437G/Alikely benign
rs1865457613:49,321,481G/Auncertain significance
rs24708784433:49,321,490G/Auncertain significance
rs20470732943:49,321,908T/Cuncertain significance
rs3696663643:49,321,930T/Cuncertain significance
rs1475329143:49,321,998C/Guncertain significance
rs23044423:49,322,027T/Aintron variant
rs7680567423:49,322,313C/Tuncertain significance
rs24708814653:49,323,555C/Tuncertain significance
rs7611147773:49,323,560G/Cuncertain significance
rs2007304743:49,323,658C/Auncertain significance
rs20470895523:49,323,662C/Tuncertain significance
rs14724905483:49,323,732G/Cuncertain significance
rs7487631353:49,323,747C/Tuncertain significance
rs73743753:49,324,455A/G
rs98110473:49,328,833A/G
rs1491314373:49,330,026T/Clikely benign
rs2006667143:49,331,846C/Guncertain significance
rs93114403:49,331,864T/Cbenign
rs1405467983:49,331,950T/Alikely benign
rs7629198393:49,331,999G/Auncertain significance
rs753944223:49,333,079T/Cregulatory region variant
rs353953473:49,334,797A/Gregulatory region variant
rs7465747863:49,336,023C/Tuncertain significance
rs7476328583:49,336,032C/Tuncertain significance
rs14684044793:49,336,044C/Tuncertain significance
rs7502699073:49,336,064C/Tuncertain significance
rs5369814483:49,339,873G/Auncertain significance
rs9249381613:49,339,887T/Cuncertain significance
rs15594706753:49,339,957C/Tuncertain significance
rs3711446803:49,343,202G/Tlikely benign
rs2003754973:49,343,212T/Cuncertain significance
rs11823292973:49,343,224A/Cuncertain significance
rs1499727553:49,346,980C/Tintron variant
rs24709209933:49,348,144T/Cuncertain significance
rs1498372793:49,348,949C/Guncertain significance
rs7771546093:49,349,028T/Cuncertain significance
rs5335219023:49,362,430G/Auncertain significance
rs14556855203:49,363,170T/Auncertain significance
rs11928326853:49,363,175T/Cuncertain significance
rs1507729953:49,363,239C/Tuncertain significance
rs341424923:49,363,759A/C
rs124975693:49,364,830G/Aintron variant
rs3759898703:49,365,128G/Alikely benign
rs1430744293:49,365,166G/Tuncertain significance
rs5367453813:49,365,180G/Auncertain significance
rs20476594913:49,372,919T/Guncertain significance
rs7662935493:49,372,958T/Cuncertain significance
rs7630792153:49,377,388T/Cuncertain significance
rs24709712003:49,377,389T/Guncertain significance
rs14865473703:49,377,414G/Cuncertain significance
rs1435335933:49,377,436G/Auncertain significance
rs1999488243:49,377,453G/Auncertain significance
rs1839775183:49,378,793A/Tupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.