VPS13A

vacuolar protein sorting 13 homolog A

Summary

The protein encoded by this gene may control steps in the cycling of proteins through the trans-Golgi network to endosomes, lysosomes and the plasma membrane. Mutations in this gene cause the autosomal recessive disorder, chorea-acanthocytosis. Alternative splicing of this gene results in multiple transcript variants. [provided by RefSeq, Jul 2008]

Known Variants2,548 total

rsidPosition (GRCh37)AllelesClassClinVar
rs123403779:79,792,019C/Gbenign
rs123492519:79,792,075G/Cbenign
rs3712926259:79,792,206T/Clikely benign
rs5426796919:79,792,357G/Cuncertain significance
rs5450924969:79,792,389G/Cuncertain significance
rs123493899:79,792,438G/Auncertain significance
rs1174887269:79,792,440A/Gbenign
rs10575156449:79,792,463G/Cuncertain significance
rs5604453009:79,792,471C/Tuncertain significance
rs5556950299:79,792,473C/Tuncertain significance
rs3723600769:79,792,605A/Tuncertain significance
rs21310299469:79,792,621A/Tlikely pathogenic
rs18237189409:79,792,629C/Tlikely benign
rs12379758309:79,792,632G/Alikely benign
rs21310300079:79,792,634C/Alikely pathogenic
rs7559719919:79,792,641C/Glikely benign
rs1436172699:79,792,644G/Alikely benign
rs3770247719:79,792,656C/Tlikely benign
rs21310301009:79,792,662C/Tlikely benign
rs21310301849:79,792,683C/Tlikely benign
rs13602458339:79,792,684T/Clikely benign
rs7454492989:79,792,692G/Alikely benign
rs12467831349:79,792,695C/Tlikely benign
rs14681446149:79,792,704T/Alikely benign
rs13137563299:79,792,707G/Alikely benign
rs15646087479:79,792,710C/Tlikely benign
rs21310303589:79,792,728G/Clikely benign
rs21310303719:79,792,729G/Clikely benign
rs25374499469:79,792,736C/Tlikely benign
rs3761530959:79,792,739C/Tlikely benign
rs3689601169:79,792,740C/Tlikely benign
rs454638979:79,792,920G/Tbenign
rs1148033289:79,792,945G/Abenign
rs111453249:79,800,111G/Cregulatory region variant
rs125515809:79,814,565C/Tbenign
rs1393794909:79,814,666T/Glikely benign
rs125528989:79,814,799A/Gbenign
rs9900612439:79,814,844T/Glikely benign
rs2020242249:79,814,847T/Gconflicting classifications of pathogenicity
rs10436641649:79,814,848T/Alikely benign
rs1906845349:79,814,854T/Clikely benign
rs25375167769:79,814,855T/Glikely benign
rs7621674659:79,814,857T/Clikely benign
rs18252286529:79,814,874C/Tlikely benign
rs9601357889:79,814,876A/Guncertain significance
rs1405187719:79,814,886A/Cuncertain significance
rs25375169579:79,814,892A/Glikely benign
rs3769522439:79,814,898T/Clikely benign
rs10256565389:79,814,901C/Tlikely benign
rs14505057529:79,814,902C/Tlikely benign
rs25375170029:79,814,905G/Cpathogenic
rs21311034559:79,814,907A/Guncertain significance
rs21311034719:79,814,914G/Clikely benign
rs7536837979:79,814,918A/Clikely benign
rs1828617709:79,814,919T/Cbenign
rs111453299:79,815,140T/Cbenign
rs1467959979:79,816,075A/Glikely benign
rs7546619809:79,816,262A/Glikely benign
rs25375215559:79,816,267A/Clikely benign
rs25375215659:79,816,268A/Tlikely benign
rs5730087089:79,816,277G/Tlikely benign
rs14470021419:79,816,279A/Tpathogenic
rs1500343229:79,816,286A/Glikely benign
rs10575156459:79,816,295A/Gconflicting classifications of pathogenicity
rs21311081639:79,816,298A/Glikely benign
rs2014904079:79,816,308A/Cuncertain significance
rs18253223529:79,816,310A/Glikely benign
rs13964796249:79,816,331A/Glikely benign
rs18253233849:79,816,332T/Clikely benign
rs7584107819:79,816,337A/Glikely benign
rs25375218749:79,816,339T/Clikely benign
rs1174787209:79,816,489T/Clikely benign
rs5384173639:79,820,213T/Clikely benign
rs7749008999:79,820,215C/Tlikely benign
rs12992469659:79,820,216C/Glikely benign
rs11754083319:79,820,217A/Clikely benign
rs25375358269:79,820,222A/Tlikely benign
rs25375358459:79,820,224T/Clikely benign
rs13124251469:79,820,227A/Glikely pathogenic
rs14515811739:79,820,237A/Guncertain significance
rs13355054179:79,820,251A/Glikely benign
rs12830586149:79,820,260C/Tlikely benign
rs15899939549:79,820,267A/Tuncertain significance
rs1154435729:79,820,269T/Cbenign
rs7515858529:79,820,284C/Tlikely benign
rs21311231809:79,820,287A/Glikely benign
rs1194770529:79,820,310T/Amissense variantpathogenic
rs9499095079:79,820,320T/Clikely benign
rs21311232959:79,820,326T/Glikely pathogenic
rs21311233219:79,820,333A/Clikely benign
rs11855922159:79,820,337T/Alikely benign
rs9775665409:79,820,338A/Tlikely benign
rs1462997169:79,820,437A/Glikely benign
rs625731719:79,820,439A/Gbenign
rs1451021749:79,820,530T/Glikely benign
rs70324089:79,820,593C/Tbenign
rs25375387399:79,820,876T/Alikely benign
rs25375387549:79,820,877T/Clikely benign
rs25375387639:79,820,879T/Clikely benign
rs12346943759:79,820,887C/Tlikely benign

Showing 100 of 2,548 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.