XRCC1

X-ray repair cross complementing 1

Summary

The protein encoded by this gene is involved in the efficient repair of DNA single-strand breaks formed by exposure to ionizing radiation and alkylating agents. This protein interacts with DNA ligase III, polymerase beta and poly (ADP-ribose) polymerase to participate in the base excision repair pathway. It may play a role in DNA processing during meiogenesis and recombination in germ cells. A rare microsatellite polymorphism in this gene is associated with cancer in patients of varying radiosensitivity. [provided by RefSeq, Jul 2008]

Known Variants93 total

rsidPosition (GRCh37)AllelesClassClinVar
rs268255819:44,047,316C/T
rs354719:44,047,550T/Cbenign
rs20196771219:44,047,554G/Auncertain significance
rs251364393219:44,047,564C/Tuncertain significance
rs19987620519:44,047,624G/Auncertain significance
rs75528192819:44,047,656G/Auncertain significance
rs14065517019:44,047,814G/Auncertain significance
rs74848543519:44,047,819C/Tuncertain significance
rs36849691019:44,047,823T/Guncertain significance
rs230718219:44,047,839C/Tlikely benign
rs230716619:44,048,330G/Amissense variant
rs230716719:44,048,332C/Tlikely benign
rs104499900219:44,048,351C/Tuncertain significance
rs75941081719:44,048,395G/Clikely benign
rs75446047019:44,049,986T/Clikely benign
rs4156181719:44,050,009G/Tuncertain significance
rs74743122419:44,050,041C/Guncertain significance
rs2547919:44,050,195C/Tbenign
rs76263345019:44,050,206C/Guncertain significance
rs230718419:44,050,231G/Tuncertain significance
rs126269242319:44,050,766G/Alikely benign
rs155576815419:44,050,780G/Apathogenic
rs74877789919:44,050,798C/Tuncertain significance
rs138074749119:44,050,863G/Auncertain significance
rs76156426219:44,051,036C/Gmissense variantpathogenic
rs230717919:44,051,108A/Tlikely benign
rs285450219:44,053,542G/T
rs2548719:44,055,726T/Cmissense variantdrug response
rs20033220719:44,055,760C/Tuncertain significance
rs20118583919:44,055,843G/Cbenign
rs2548619:44,055,898C/Tdownstream gene variant
rs37756628119:44,056,235C/Tuncertain significance
rs57445091119:44,056,236G/Alikely pathogenic
rs251365017619:44,056,270C/Glikely benign
rs230717319:44,056,273C/Abenign
rs2549119:44,056,326G/Auncertain significance
rs92996716819:44,056,338C/Tuncertain significance
rs2549019:44,056,341T/Cbenign
rs321336619:44,056,351T/Clikely benign
rs20052860119:44,056,352C/Tconflicting classifications of pathogenicity
rs90401752719:44,056,371C/Tuncertain significance
rs75723806619:44,056,382C/Tuncertain significance
rs14616866219:44,056,400G/Alikely benign
rs2548919:44,056,412C/Tmissense variantassociation
rs14391728619:44,056,954G/Alikely benign
rs76165022219:44,057,059G/Auncertain significance
rs36883775719:44,057,148C/Tuncertain significance
rs56292614719:44,057,178A/Clikely benign
rs91592719:44,057,227T/Gsynonymous variantbenign
rs179978019:44,057,276G/Aassociation
rs179978219:44,057,574G/Amissense variantbenign
rs230717019:44,057,584G/Clikely benign
rs19056310919:44,057,610C/Tlikely benign
rs14918792519:44,057,767C/Tbenign
rs230719119:44,057,768G/Abenign
rs26760552619:44,057,828G/Cuncertain significance
rs20200616819:44,058,790C/Tlikely benign
rs75146308719:44,058,808G/Auncertain significance
rs36891171919:44,058,813G/Alikely benign
rs75222429219:44,058,830C/Guncertain significance
rs77736556119:44,058,832C/Tuncertain significance
rs14388184519:44,058,860G/Auncertain significance
rs222848719:44,058,892C/Tlikely benign
rs95086220919:44,058,914G/Auncertain significance
rs20037659419:44,058,921G/Alikely benign
rs137516127219:44,058,926G/Auncertain significance
rs20014676919:44,058,928G/Tuncertain significance
rs285450119:44,060,001A/T
rs321334419:44,060,653G/A
rs321333719:44,061,937T/C
rs321333219:44,062,687G/T
rs53861579419:44,063,431C/T
rs53734919419:44,063,484A/C
rs5641256419:44,064,325G/Adownstream gene variant
rs91533764519:44,065,063T/Cuncertain significance
rs77513518019:44,065,066T/Cuncertain significance
rs4155831319:44,065,083G/Abenign
rs53723685919:44,065,100C/Auncertain significance
rs2549619:44,065,102A/Gbenign
rs19958974919:44,065,115C/Tlikely benign
rs230717419:44,065,167C/Tlikely benign
rs57776311119:44,066,400T/G
rs202109219:44,068,706T/Cintron variant
rs1261108819:44,072,802G/Aintron variant
rs285450919:44,074,597T/A
rs321325519:44,077,507G/Aupstream gene variant
rs230718619:44,079,591C/Alikely benign
rs230718719:44,079,611G/Abenign
rs321324519:44,079,687G/Tcoding sequence variant
rs19302081719:44,081,285C/Aupstream gene variant
rs268258519:44,081,288A/C
rs11202759119:44,081,452G/Aupstream gene variant
rs11377989319:44,081,676G/Aupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.