ACVR2A

activin A receptor type 2A

Summary

This gene encodes a receptor that mediates the functions of activins, which are members of the transforming growth factor-beta (TGF-beta) superfamily involved in diverse biological processes. The encoded protein is a transmembrane serine-threonine kinase receptor which mediates signaling by forming heterodimeric complexes with various combinations of type I and type II receptors and ligands in a cell-specific manner. The encoded type II receptor is primarily involved in ligand-binding and includes an extracellular ligand-binding domain, a transmembrane domain and a cytoplasmic serine-threonine kinase domain. This gene may be associated with susceptibility to preeclampsia, a pregnancy-related disease which can result in maternal and fetal morbidity and mortality. Alternative splicing results in multiple transcript variants of this gene. [provided by RefSeq, Jun 2013]

Known Variants20 total

rsidPosition (GRCh37)AllelesClassClinVar
rs14249542:148,600,794G/Aupstream gene variant
rs798611722:148,607,438G/Aintron variant
rs10140642:148,612,154A/C
rs177419782:148,617,380C/Gintron variant
rs130219722:148,631,232A/Tupstream gene variant
rs75599252:148,640,930T/Cintron variant
rs14249412:148,643,118C/A
rs21619832:148,649,386G/Aintron variant
rs7765427122:148,653,960C/Tuncertain significance
rs24677755422:148,657,044A/Guncertain significance
rs24677763222:148,657,331C/Guncertain significance
rs1463834182:148,657,423A/Guncertain significance
rs37686872:148,672,020C/Tintron variant
rs14894994692:148,672,898A/Guncertain significance
rs5624644672:148,674,960G/Auncertain significance
rs24678086952:148,676,094G/Cuncertain significance
rs15588144732:148,677,831A/Cuncertain significance
rs16874210112:148,680,552G/Auncertain significance
rs2020500642:148,684,782T/Cuncertain significance
rs7654085862:148,684,784G/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.