AKAP13

A-kinase anchoring protein 13

Summary

The A-kinase anchor proteins (AKAPs) are a group of structurally diverse proteins which have the common function of binding to the regulatory subunit of protein kinase A (PKA) and confining the holoenzyme to discrete locations within the cell. This gene encodes a member of the AKAP family. Alternative splicing of this gene results in multiple transcript variants encoding different isoforms containing c-terminal dbl oncogene homology (DH) and pleckstrin homology (PH) domains. The DH domain is associated with guanine nucleotide exchange activation for the Rho/Rac family of small GTP binding proteins, resulting in the conversion of the inactive GTPase to the active form capable of transducing signals. The PH domain has multiple functions. Therefore, these isoforms function as scaffolding proteins to coordinate a Rho signaling pathway, function as protein kinase A-anchoring proteins and, in addition, enhance ligand-dependent activity of estrogen receptors alpha and beta. [provided by RefSeq, Jul 2012]

Known Variants234 total

rsidPosition (GRCh37)AllelesClassClinVar
rs717746915:85,924,827A/G
rs54585832515:85,963,472T/C
rs7809888115:85,964,821C/G
rs1291729615:85,979,905C/T
rs484305915:85,997,490A/Gintron variant
rs6202211215:86,009,608T/Gintron variant
rs649718715:86,011,350A/Gintron variant
rs455199015:86,015,287A/Cintron variant
rs3555872815:86,024,111T/Cintron variant
rs3557029115:86,026,974A/Gintron variant
rs128994722015:86,064,695G/Cuncertain significance
rs77068623115:86,064,749C/Tuncertain significance
rs649604415:86,067,306G/Aintron variant
rs717025115:86,074,380C/Tregulatory region variant
rs37764346215:86,076,851G/Auncertain significance
rs37104604015:86,076,854C/Guncertain significance
rs254435857715:86,077,091G/Auncertain significance
rs254435859215:86,077,101G/Cuncertain significance
rs76775771215:86,087,015G/Auncertain significance
rs75399344915:86,087,039T/Cuncertain significance
rs77536153515:86,087,076G/Tuncertain significance
rs207764705915:86,087,084C/Auncertain significance
rs20011231315:86,087,112C/Guncertain significance
rs14611507415:86,087,167C/Guncertain significance
rs649608615:86,090,203G/Aintron variant
rs6202389115:86,097,216G/C
rs74982066515:86,118,403A/Guncertain significance
rs11421989715:86,118,415A/Cuncertain significance
rs93936372715:86,118,450G/Auncertain significance
rs77951683115:86,118,457A/Cuncertain significance
rs207896578515:86,118,469C/Guncertain significance
rs254461731215:86,118,514G/Auncertain significance
rs13922893815:86,118,517C/Guncertain significance
rs146443366315:86,118,550A/Cuncertain significance
rs102672315:86,119,326C/Tdownstream gene variant
rs102672115:86,119,420T/A
rs100290324315:86,122,213A/Guncertain significance
rs7345243015:86,122,299G/Abenign
rs75217932015:86,122,312G/Cuncertain significance
rs117786087115:86,122,432G/Auncertain significance
rs140240452415:86,122,447T/Clikely benign
rs116496831415:86,122,471C/Guncertain significance
rs20149947415:86,122,473G/Cuncertain significance
rs37703669215:86,122,494A/Guncertain significance
rs123384994815:86,122,517T/Auncertain significance
rs13968274615:86,122,529G/Abenign
rs37096483115:86,122,557A/Guncertain significance
rs207911368115:86,122,681C/Tuncertain significance
rs75918512615:86,122,785A/Tuncertain significance
rs3593005115:86,122,790G/Abenign
rs37009908615:86,122,807G/Auncertain significance
rs75939574815:86,122,866G/Auncertain significance
rs75668446915:86,122,887A/Guncertain significance
rs11538519715:86,122,909C/Tlikely benign
rs116548287315:86,122,939A/Cuncertain significance
rs99503683815:86,122,971G/Auncertain significance
rs14272655915:86,122,978C/Tuncertain significance
rs254463992815:86,122,983A/Cuncertain significance
rs254463998915:86,123,010T/Cuncertain significance
rs77770993215:86,123,020G/Tuncertain significance
rs76165624715:86,123,050A/Guncertain significance
rs5615616515:86,123,085A/Gbenign
rs76198731215:86,123,103G/Auncertain significance
rs126882121015:86,123,115C/Auncertain significance
rs74791983815:86,123,124G/Tuncertain significance
rs254464033315:86,123,140C/Tuncertain significance
rs6173184215:86,123,142A/Glikely benign
rs254464038615:86,123,160G/Alikely benign
rs11239666215:86,123,216A/Gbenign
rs11359524315:86,123,231C/Tlikely benign
rs133972726515:86,123,355A/Cuncertain significance
rs207912284615:86,123,362G/Auncertain significance
rs14653111615:86,123,489T/Auncertain significance
rs77563944515:86,123,496C/Auncertain significance
rs207912617115:86,123,634G/Auncertain significance
rs11470581515:86,123,770A/Tlikely benign
rs11470310615:86,123,809T/Clikely benign
rs407525615:86,123,833T/Glikely benign
rs20130973615:86,123,874G/Auncertain significance
rs75880505215:86,123,890G/Auncertain significance
rs14350511815:86,124,044G/Cbenign
rs143365638115:86,124,085A/Guncertain significance
rs96195825615:86,124,086T/Auncertain significance
rs14182212315:86,124,250C/Tlikely benign
rs97600823115:86,124,330G/Cuncertain significance
rs13826556915:86,124,339G/Tuncertain significance
rs207913619115:86,124,347C/Auncertain significance
rs77943619815:86,124,352T/Auncertain significance
rs74839769315:86,124,355C/Tuncertain significance
rs86680217115:86,124,453G/Tuncertain significance
rs11662242415:86,124,461C/Tlikely benign
rs484307415:86,124,483C/Gmissense variant
rs6174251515:86,124,515T/Cbenign
rs56393731415:86,124,563G/Alikely benign
rs75776423615:86,124,574C/Tuncertain significance
rs77980359615:86,124,758A/Guncertain significance
rs126789639615:86,124,765G/Auncertain significance
rs121684038115:86,124,804T/Cuncertain significance
rs11546849815:86,124,824G/Alikely benign
rs88894990115:86,124,832A/Guncertain significance

Showing 100 of 234 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.