ATF6B

activating transcription factor 6 beta

Summary

The protein encoded by this gene is a transcription factor in the unfolded protein response (UPR) pathway during ER stress. Either as a homodimer or as a heterodimer with ATF6-alpha, the encoded protein binds to the ER stress response element, interacting with nuclear transcription factor Y to activate UPR target genes. The protein is normally found in the membrane of the endoplasmic reticulum; however, under ER stress, the N-terminal cytoplasmic domain is cleaved from the rest of the protein and translocates to the nucleus. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Oct 2008]

Known Variants44 total

rsidPosition (GRCh37)AllelesClassClinVar
rs81116:32,083,175C/Tupstream gene variant
rs82836:32,083,300A/Gupstream gene variant
rs7733755186:32,083,541T/Auncertain significance
rs7588836176:32,083,568G/Tuncertain significance
rs7536187736:32,083,730C/Tuncertain significance
rs1479558786:32,084,337T/Alikely benign
rs7747028496:32,084,515C/Tuncertain significance
rs3731797836:32,084,518C/Tuncertain significance
rs1996109696:32,084,564G/Auncertain significance
rs3729666786:32,084,872G/Alikely benign
rs2007178696:32,085,092C/Tbenign
rs13533180766:32,085,155A/Guncertain significance
rs7679637876:32,085,171C/Tuncertain significance
rs2048906:32,085,598C/Tupstream gene variant
rs7734655096:32,085,663G/Alikely benign
rs12519020446:32,085,693C/Tlikely benign
rs24839289146:32,085,697G/Tuncertain significance
rs11855726926:32,085,709C/Tuncertain significance
rs11797193706:32,085,742G/Cuncertain significance
rs1423519496:32,085,795G/Auncertain significance
rs7809303866:32,085,811T/Cuncertain significance
rs13767596586:32,086,878C/Tuncertain significance
rs2021596906:32,087,609C/Guncertain significance
rs24839418406:32,087,648T/Guncertain significance
rs5559846186:32,087,688T/Guncertain significance
rs5414577456:32,088,656G/Auncertain significance
rs10312050496:32,088,777T/Cuncertain significance
rs22286286:32,088,854G/Asynonymous variant
rs1443549766:32,092,625T/Gdownstream gene variant
rs7604400166:32,093,902T/Cuncertain significance
rs7594755426:32,093,921C/Tuncertain significance
rs14491430126:32,093,935G/Tuncertain significance
rs24839796756:32,094,017C/Tuncertain significance
rs2048936:32,094,593T/Cdownstream gene variant
rs5692408116:32,095,255A/Glikely benign
rs24839895636:32,095,285A/Glikely benign
rs7469854186:32,095,455T/Auncertain significance
rs172016236:32,095,465G/Auncertain significance
rs12709882256:32,095,471G/Cuncertain significance
rs5724645486:32,095,900G/Alikely benign
rs7760583186:32,095,917C/Auncertain significance
rs7514340776:32,095,954C/Tuncertain significance
rs12163484556:32,095,980G/Auncertain significance
rs412689056:32,097,611G/Aupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.