B4GALNT2

beta-1,4-N-acetyl-galactosaminyltransferase 2 (SID blood group)

Summary

B4GALNT2 catalyzes the last step in the biosynthesis of the human Sd(a) antigen through the addition of an N-acetylgalactosamine residue via a beta-1,4 linkage to a subterminal galactose residue substituted with an alpha-2,3-linked sialic acid. B4GALNT2 also catalyzes the last step in the biosynthesis of the Cad antigen (Montiel et al., 2003 [PubMed 12678917]).[supplied by OMIM, Mar 2008]

Known Variants45 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1245018417:47,203,421G/A
rs7283540517:47,207,658C/Tupstream gene variant
rs37040664217:47,207,665G/A
rs14644371417:47,210,166C/Alikely benign
rs78033893517:47,210,413G/Auncertain significance
rs76198791817:47,210,446G/Auncertain significance
rs97785753717:47,210,464C/Tuncertain significance
rs14782761217:47,210,488G/Cuncertain significance
rs57734147417:47,218,643A/Clikely benign
rs14140580017:47,218,665T/Clikely benign
rs250913116017:47,218,721G/Cuncertain significance
rs75255437317:47,218,728C/Guncertain significance
rs97335987617:47,218,746T/Clikely benign
rs76577537217:47,218,776G/Alikely benign
rs77167976017:47,219,433C/Auncertain significance
rs56599303417:47,219,504G/Tuncertain significance
rs74977581217:47,219,506C/Guncertain significance
rs37415530817:47,219,528A/Guncertain significance
rs77068275017:47,230,254C/Tuncertain significance
rs56037390917:47,233,952C/Tuncertain significance
rs204283834417:47,236,483C/Guncertain significance
rs74815512417:47,236,532A/Guncertain significance
rs135370847617:47,236,577T/Cuncertain significance
rs37385476217:47,237,973G/Cuncertain significance
rs76408598417:47,237,980C/Guncertain significance
rs250891298617:47,241,574C/Guncertain significance
rs7283541717:47,241,642A/Gbenign
rs76696510117:47,243,535G/Tuncertain significance
rs14713210917:47,243,560G/Auncertain significance
rs5980994917:47,245,929C/Tupstream gene variant
rs14844123717:47,246,074A/Gaffects
rs722488817:47,246,163T/Cbenign
rs56408982417:47,246,223G/Cuncertain significance
rs11274095417:47,246,247C/Tbenign
rs75500365217:47,246,917G/Auncertain significance
rs121161785917:47,246,930C/Tuncertain significance
rs6174361717:47,246,956T/Cbenign
rs75543786317:47,246,993A/Guncertain significance
rs204294365617:47,246,999C/Tuncertain significance
rs132463904617:47,247,047T/Cuncertain significance
rs130337590517:47,247,059A/Guncertain significance
rs20130719117:47,247,086C/Tuncertain significance
rs2868996817:47,247,257C/Tdownstream gene variant
rs182984517:47,248,391A/Gdownstream gene variant
rs14047314917:47,250,444C/Gcoding sequence variant

Gene information from NCBI Gene. Variant classifications from ClinVar.