BTN2A1

butyrophilin subfamily 2 member A1

Summary

This gene encodes a member of the immunoglobulin superfamily. The gene is located in a cluster of butyrophilin-like genes in the juxta-telomeric region of the major histocompatibility complex on chromosome 6. A pseudogene of this gene has been identified in this cluster. The encoded protein is an integral plasma membrane protein involved in lipid, fatty-acid, and sterol metabolism. Alterations in this gene may be associated with several disease states including metabolic syndrome. Multiple alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2013]

Known Variants50 total

rsidPosition (GRCh37)AllelesClassClinVar
rs69298466:26,458,265T/Cregulatory region variant
rs7715436006:26,458,888C/Auncertain significance
rs7605366336:26,458,895C/Tuncertain significance
rs7772618456:26,459,807G/Auncertain significance
rs3719443356:26,459,820G/Auncertain significance
rs1460863346:26,459,864G/Tuncertain significance
rs7711006556:26,459,899G/Cuncertain significance
rs1413122576:26,459,946G/Tuncertain significance
rs2005355076:26,459,961T/Cuncertain significance
rs3690331886:26,460,015G/Auncertain significance
rs3738258186:26,460,026G/Auncertain significance
rs7460986346:26,460,035A/Guncertain significance
rs17632153626:26,463,507C/Tuncertain significance
rs9192375546:26,463,551G/Tuncertain significance
rs7814779076:26,463,588G/Alikely benign
rs1397737636:26,463,598C/Tlikely benign
rs14052073046:26,463,622T/Clikely benign
rs1443583496:26,463,636G/Auncertain significance
rs1387270766:26,463,692G/Auncertain significance
rs7709520346:26,463,720G/Alikely benign
rs7758380406:26,463,729A/Guncertain significance
rs725008186:26,463,778C/Tintron variant
rs25333448796:26,465,448G/Auncertain significance
rs7749002746:26,465,490G/Alikely benign
rs10411651666:26,465,518A/Cuncertain significance
rs5323881076:26,465,530A/Guncertain significance
rs1481552276:26,465,559C/Tuncertain significance
rs1402811086:26,465,572A/Guncertain significance
rs3697482356:26,465,577G/Tuncertain significance
rs1442323726:26,465,580C/Glikely benign
rs7483766816:26,465,601C/Tuncertain significance
rs7705229736:26,466,302C/Tuncertain significance
rs19771996:26,466,389G/Aintron variant
rs1167827266:26,468,201C/Tbenign
rs1996019426:26,468,301G/Auncertain significance
rs1404844806:26,468,314G/Cuncertain significance
rs1456626746:26,468,316G/Auncertain significance
rs37345426:26,468,326G/Amissense variant
rs7507036406:26,468,332G/Tuncertain significance
rs3690082046:26,468,336C/Guncertain significance
rs7650227776:26,468,337G/Auncertain significance
rs7515506176:26,468,358G/Auncertain significance
rs13287772286:26,468,392T/Auncertain significance
rs1999206146:26,468,479G/Auncertain significance
rs5653175406:26,468,488G/Auncertain significance
rs2019965426:26,468,547G/Alikely benign
rs2014119176:26,468,562G/Auncertain significance
rs7462787436:26,468,595G/Auncertain significance
rs13552053706:26,468,650C/Auncertain significance
rs2001264686:26,468,678C/Guncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.