CAPZB

capping actin protein of muscle Z-line subunit beta

Summary

This gene encodes the beta subunit of the barbed-end actin binding protein, which belongs to the F-actin capping protein family. The capping protein is a heterodimeric actin capping protein that blocks actin filament assembly and disassembly at the fast growing (barbed) filament ends and functions in regulating actin filament dynamics as well as in stabilizing actin filament lengths in muscle and nonmuscle cells. A pseudogene of this gene is located on the long arm of chromosome 2. Multiple alternatively spliced transcript variants encoding different isoforms have been found.[provided by RefSeq, Aug 2013]

Known Variants24 total

rsidPosition (GRCh37)AllelesClassClinVar
rs3680778671:19,669,284C/Tuncertain significance
rs11658079751:19,669,332T/Cuncertain significance
rs7517642911:19,669,356G/Cuncertain significance
rs5631450811:19,681,525C/T
rs3731707691:19,683,225G/Alikely benign
rs5327319721:19,683,226G/Auncertain significance
rs7502559321:19,683,927C/Tuncertain significance
rs2143091:19,692,334G/C
rs2143101:19,692,697T/Cintron variant
rs25222226721:19,705,043T/Cuncertain significance
rs76671:19,718,824G/Aintron variant
rs49120851:19,729,087G/Cintron variant
rs124030411:19,730,927A/Gintron variant
rs92870471:19,736,534T/Cregulatory region variant
rs1470950591:19,746,151G/Alikely benign
rs120277021:19,747,103G/Tupstream gene variant
rs715129471:19,749,550C/G
rs49119921:19,750,486T/Aupstream gene variant
rs120454401:19,765,518T/Gintron variant
rs124070891:19,767,814G/Cintron variant
rs1144584711:19,769,930T/Aintron variant
rs589520601:19,774,582G/Aintron variant
rs124093011:19,774,715G/Aintron variant
rs39134391:19,780,509C/A

Gene information from NCBI Gene. Variant classifications from ClinVar.