CD46

CD46 molecule

Summary

The protein encoded by this gene is a type I membrane protein and is a regulatory part of the complement system. The encoded protein has cofactor activity for inactivation of complement components C3b and C4b by serum factor I, which protects the host cell from damage by complement. In addition, the encoded protein can act as a receptor for the Edmonston strain of measles virus, human herpesvirus-6, and type IV pili of pathogenic Neisseria. Finally, the protein encoded by this gene may be involved in the fusion of the spermatozoa with the oocyte during fertilization. Mutations at this locus have been associated with susceptibility to hemolytic uremic syndrome. Alternatively spliced transcript variants encoding different isoforms have been described. [provided by RefSeq, Jun 2010]

Known Variants302 total

rsidPosition (GRCh37)AllelesClassClinVar
rs27962671:207,924,906G/Abenign
rs27962681:207,925,192A/Gbenign
rs412663971:207,925,361C/Gbenign
rs10238946251:207,925,431A/Guncertain significance
rs744770321:207,925,547C/Alikely benign
rs9315671001:207,925,548C/Tuncertain significance
rs8860458361:207,925,552C/Tuncertain significance
rs13356245341:207,925,567C/Tuncertain significance
rs3756719741:207,925,568C/Tuncertain significance
rs7565804331:207,925,569C/Tlikely benign
rs16549863301:207,925,572C/Alikely benign
rs7497966691:207,925,574G/Tuncertain significance
rs7748288391:207,925,587C/Glikely benign
rs14181061161:207,925,592C/Tuncertain significance
rs1388438161:207,925,595C/Tlikely benign
rs16549936961:207,925,597T/Cuncertain significance
rs7601657791:207,925,609G/Auncertain significance
rs16549994891:207,925,614G/Tuncertain significance
rs25263375081:207,925,615C/Tuncertain significance
rs12388616561:207,925,616T/Cuncertain significance
rs21025122111:207,925,622C/Auncertain significance
rs7658707211:207,925,625C/Guncertain significance
rs7503428651:207,925,627A/Gconflicting classifications of pathogenicity
rs12954056231:207,925,628T/Cuncertain significance
rs7650475961:207,925,629G/Auncertain significance
rs7802609591:207,925,646C/Guncertain significance
rs14364908701:207,925,653C/Tuncertain significance
rs21025126451:207,925,654G/Cconflicting classifications of pathogenicity
rs10137940721:207,925,659G/Tuncertain significance
rs7794463811:207,925,661C/Tlikely benign
rs13742342421:207,925,662C/Tlikely benign
rs25263391021:207,925,664C/Tlikely benign
rs120674601:207,930,167T/Abenign
rs27243841:207,930,203G/Aintron variantbenign
rs14419370531:207,930,358G/Cpathogenic
rs15715781261:207,930,362C/Tuncertain significance
rs1219095911:207,930,365G/Amissense variantpathogenic
rs14173338031:207,930,370G/Auncertain significance
rs7539247201:207,930,379A/Guncertain significance
rs13046310271:207,930,389C/Tuncertain significance
rs5649108681:207,930,391A/Cconflicting classifications of pathogenicity
rs25263992801:207,930,393G/Auncertain significance
rs13614373491:207,930,423T/Clikely benign
rs25263999281:207,930,427A/Guncertain significance
rs7466639341:207,930,428T/Cuncertain significance
rs7779660421:207,930,430G/Auncertain significance
rs1219095901:207,930,436C/Tstop gainedpathogenic
rs7806935191:207,930,437G/Auncertain significance
rs13357487541:207,930,440T/Cuncertain significance
rs25264004701:207,930,444T/Auncertain significance
rs7453178561:207,930,446A/Guncertain significance
rs16556333531:207,930,452G/Auncertain significance
rs1504299801:207,930,459A/Tconflicting classifications of pathogenicity
rs13272317771:207,930,477T/Glikely benign
rs25264018921:207,930,478C/Tuncertain significance
rs25264019361:207,930,479C/Tuncertain significance
rs25264020361:207,930,481C/Tuncertain significance
rs7685383721:207,930,485C/Tuncertain significance
rs25264021721:207,930,491A/Guncertain significance
rs25264022941:207,930,496A/Gconflicting classifications of pathogenicity
rs2001336311:207,930,505C/Tuncertain significance
rs7610008461:207,930,506G/Auncertain significance
rs10477804831:207,930,512A/Tuncertain significance
rs2015205671:207,930,516A/Glikely benign
rs25264027411:207,930,518G/Apathogenic
rs1153857121:207,930,522A/Glikely benign
rs25264029601:207,930,529T/Guncertain significance
rs1483834991:207,930,537C/Tconflicting classifications of pathogenicity
rs5472983941:207,930,538G/Tuncertain significance
rs25264033411:207,930,539C/Tuncertain significance
rs1120895941:207,930,546T/Cconflicting classifications of pathogenicity
rs14198986301:207,930,548G/Cpathogenic
rs7697422941:207,930,549T/Gpathogenic
rs14295629161:207,930,868A/Glikely benign
rs7598130891:207,930,883A/Gpathogenic
rs1168001261:207,930,891C/Tconflicting classifications of pathogenicity
rs16557005811:207,930,902A/Guncertain significance
rs11745770311:207,930,928A/Glikely benign
rs14208879271:207,930,933C/Tuncertain significance
rs7576760221:207,930,946T/Glikely benign
rs9998216081:207,930,949C/Tlikely benign
rs25264112301:207,930,965A/Tuncertain significance
rs3760911141:207,930,968C/Tuncertain significance
rs5541423241:207,930,973T/Clikely benign
rs21025421291:207,930,988G/Alikely pathogenic
rs25264117661:207,931,000T/Glikely benign
rs24665731:207,931,175T/Gbenign
rs7785478741:207,932,965C/Tlikely benign
rs21025523921:207,932,978A/Glikely benign
rs15532505681:207,932,996T/Guncertain significance
rs25264367511:207,933,005A/Glikely benign
rs121260881:207,933,011G/Alikely benign
rs16559669191:207,933,012T/Cuncertain significance
rs3711068851:207,933,018G/Cuncertain significance
rs1450411581:207,933,047C/Tbenign
rs3741756121:207,933,048G/Auncertain significance
rs7735713151:207,933,060A/Guncertain significance
rs21025528651:207,933,063T/Cconflicting classifications of pathogenicity
rs413170811:207,933,353A/Gbenign
rs24665721:207,934,487A/Cbenign

Showing 100 of 302 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.