CTSH

cathepsin H

Summary

The protein encoded by this gene is a lysosomal cysteine proteinase important in the overall degradation of lysosomal proteins. It is composed of a dimer of disulfide-linked heavy and light chains, both produced from a single protein precursor. The encoded protein, which belongs to the peptidase C1 protein family, can act both as an aminopeptidase and as an endopeptidase. Increased expression of this gene has been correlated with malignant progression of prostate tumors. Alternate splicing of this gene results in multiple transcript variants encoding different isoforms. [provided by RefSeq, Jan 2016]

Known Variants36 total

rsidPosition (GRCh37)AllelesClassClinVar
rs53824087615:79,213,063T/G
rs1155839715:79,214,531G/Alikely benign
rs76794849615:79,214,534C/Tuncertain significance
rs228969115:79,215,238T/Cintron variant
rs75037115515:79,215,338T/Auncertain significance
rs74827280715:79,215,367T/Guncertain significance
rs228969415:79,217,606G/Aintron variant
rs250519029815:79,217,697T/Cuncertain significance
rs13884405715:79,217,704T/Cuncertain significance
rs14821987515:79,220,054C/Tlikely benign
rs37560133815:79,220,113C/Auncertain significance
rs14683616115:79,223,833C/Tuncertain significance
rs228970015:79,224,683C/G
rs75837757715:79,224,731C/Tuncertain significance
rs14321496415:79,224,743C/Tuncertain significance
rs14502966315:79,227,417G/Auncertain significance
rs77102698715:79,228,026G/Auncertain significance
rs20094043215:79,228,072C/Guncertain significance
rs13841972015:79,229,679A/Gbenign
rs143804825015:79,229,680T/Cuncertain significance
rs75266478415:79,229,683T/Cuncertain significance
rs14405769415:79,229,691G/Alikely benign
rs54434036715:79,229,700C/Tlikely benign
rs980643915:79,229,745C/Tbenign
rs1015286815:79,230,969A/Gintron variant
rs7881342315:79,231,005T/Cregulatory region variant
rs6201322715:79,231,046G/Tregulatory region variant
rs3459343915:79,234,957G/Aintron variant
rs382593215:79,235,446T/Cregulatory region variant
rs18847013415:79,236,217G/Cintron variant
rs103693715:79,237,180C/Aregulatory region variant
rs3500143115:79,237,257C/Tbenign
rs159629589315:79,237,261A/Clikely benign
rs54505169815:79,237,291C/Tbenign
rs156738700315:79,237,295G/Auncertain significance
rs137836994015:79,237,304A/Guncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.