DGCR8

DGCR8 microprocessor complex subunit

Summary

This gene encodes a subunit of the microprocessor complex which mediates the biogenesis of microRNAs from the primary microRNA transcript. The encoded protein is a double-stranded RNA binding protein that functions as the non-catalytic subunit of the microprocessor complex. This protein is required for binding the double-stranded RNA substrate and facilitates cleavage of the RNA by the ribonuclease III protein, Drosha. Alternate splicing results in multiple transcript variants. [provided by RefSeq, Jun 2010]

Known Variants70 total

rsidPosition (GRCh37)AllelesClassClinVar
rs36870599422:20,073,519G/Alikely benign
rs14078233422:20,073,529G/Auncertain significance
rs20101106522:20,073,560G/Auncertain significance
rs134629309922:20,073,563C/Guncertain significance
rs11166952722:20,073,564C/Tlikely benign
rs77641576722:20,073,572C/Tuncertain significance
rs76250536822:20,073,580C/Tuncertain significance
rs129813399022:20,073,683C/Guncertain significance
rs135656662522:20,073,695A/Guncertain significance
rs131174519322:20,073,737G/Auncertain significance
rs75515878922:20,073,774G/Alikely benign
rs77515521622:20,073,792A/Glikely benign
rs37770684622:20,073,824A/Guncertain significance
rs37248345222:20,073,861C/Tlikely benign
rs37035095722:20,073,915C/Tlikely benign
rs19259887522:20,073,924G/Alikely benign
rs13833220722:20,073,930C/Tbenign
rs53694958722:20,073,996C/Tlikely benign
rs55592259922:20,074,000G/Tuncertain significance
rs19975395022:20,074,090T/Guncertain significance
rs251926426022:20,074,166G/Tuncertain significance
rs729155222:20,074,699C/Tbenign
rs76582084122:20,074,785C/Tuncertain significance
rs20139375822:20,074,819G/Cuncertain significance
rs11714834222:20,076,642G/Adownstream gene variant
rs77952082122:20,077,504C/Tlikely benign
rs14339090222:20,077,566G/Alikely benign
rs14588513622:20,077,575G/Alikely benign
rs37224772122:20,077,595G/Auncertain significance
rs77877891922:20,077,610G/Auncertain significance
rs75995893422:20,077,642G/Cuncertain significance
rs204953723922:20,077,686C/Tuncertain significance
rs56091086522:20,077,689C/Guncertain significance
rs3420410122:20,077,720A/Cbenign
rs11389161822:20,077,756C/Tbenign
rs156895447922:20,077,757G/Auncertain significance
rs77734877922:20,077,778G/Auncertain significance
rs14249718322:20,078,948T/Clikely benign
rs36901860022:20,078,990C/Tuncertain significance
rs78068355722:20,079,013T/Clikely benign
rs75086805722:20,079,014G/Cuncertain significance
rs77915147922:20,079,068C/Tuncertain significance
rs138386668522:20,079,069G/Auncertain significance
rs77212467622:20,079,079G/Clikely benign
rs14933667522:20,079,084C/Guncertain significance
rs78069289122:20,079,423G/Alikely benign
rs1108932822:20,079,603A/T
rs204958246122:20,080,412C/Tuncertain significance
rs19245646122:20,080,839A/Cintron variant
rs37691726622:20,082,229T/Clikely benign
rs251928105522:20,082,284C/Guncertain significance
rs3556974722:20,082,293A/Glikely benign
rs960625022:20,090,192A/Tintron variant
rs163341822:20,091,756T/G
rs11236753322:20,091,833G/Aintron variant
rs14597050722:20,093,738C/Tlikely benign
rs20189257722:20,094,185G/Cuncertain significance
rs13984299622:20,094,193G/Alikely benign
rs123497393522:20,094,806G/Auncertain significance
rs14667877022:20,094,825C/Tlikely benign
rs77378340922:20,094,896G/Auncertain significance
rs736413222:20,096,172G/Aregulatory region variant
rs20147624722:20,097,575T/Auncertain significance
rs75048456322:20,097,580T/Clikely benign
rs14888425722:20,097,585C/Tconflicting classifications of pathogenicity
rs76511305022:20,097,586G/Alikely benign
rs99763910822:20,097,601C/Tlikely benign
rs20097269822:20,097,602G/Auncertain significance
rs164029922:20,098,359T/Gcoding sequence variant
rs41730922:20,098,544G/Acoding sequence variantbenign

Gene information from NCBI Gene. Variant classifications from ClinVar.