EDEM2

ER degradation enhancing alpha-mannosidase like protein 2

Summary

In the endoplasmic reticulum (ER), misfolded proteins are retrotranslocated to the cytosol and degraded by the proteasome in a process known as ER-associated degradation (ERAD). EDEM2 belongs to a family of proteins involved in ERAD of glycoproteins (Mast et al., 2005 [PubMed 15537790]).[supplied by OMIM, Mar 2008]

Known Variants41 total

rsidPosition (GRCh37)AllelesClassClinVar
rs14971357920:33,703,381G/Auncertain significance
rs77806618520:33,703,387G/Tuncertain significance
rs74726645520:33,703,388C/Tlikely benign
rs77811728920:33,703,454A/Tuncertain significance
rs14558649220:33,703,523C/Tuncertain significance
rs251547264220:33,703,552T/Cuncertain significance
rs75622267720:33,703,591T/Cuncertain significance
rs374642920:33,703,607C/Tmissense variant
rs76670090520:33,703,647G/Cuncertain significance
rs52724850020:33,703,701G/Abenign
rs74543237520:33,703,703G/Auncertain significance
rs56866690620:33,706,474G/Auncertain significance
rs37526445020:33,706,492C/Tuncertain significance
rs37067359620:33,706,516A/Guncertain significance
rs75361504020:33,711,716C/Tuncertain significance
rs133904632820:33,711,723C/Guncertain significance
rs251548396320:33,711,780A/Guncertain significance
rs125449439020:33,711,829A/Cuncertain significance
rs13843855320:33,711,830A/Guncertain significance
rs614230220:33,713,251A/Gintron variant
rs20167384020:33,714,106G/Auncertain significance
rs37717596020:33,719,460T/Auncertain significance
rs612084420:33,720,240G/Tintron variant
rs36832121620:33,722,573G/Auncertain significance
rs13978056920:33,722,587C/Guncertain significance
rs75951473320:33,722,608G/Auncertain significance
rs77558660720:33,722,693G/Tuncertain significance
rs251550346420:33,722,732T/Cuncertain significance
rs229588820:33,722,863A/Gintron variant
rs612084820:33,728,678T/Cintron variant
rs123185561420:33,730,199G/Cuncertain significance
rs36975326720:33,730,224C/Tuncertain significance
rs251551531920:33,730,280A/Guncertain significance
rs612084920:33,730,387C/Tintron variant
rs7789344620:33,730,549T/Aintron variant
rs97658088520:33,732,799C/Tuncertain significance
rs119025513020:33,734,970T/Auncertain significance
rs15031412520:33,734,989G/Cuncertain significance
rs251552394820:33,735,024C/Auncertain significance
rs75122203520:33,735,051C/Auncertain significance
rs606026920:33,736,515C/T

Gene information from NCBI Gene. Variant classifications from ClinVar.