GLS2

glutaminase 2

Summary

The protein encoded by this gene is a mitochondrial phosphate-activated glutaminase that catalyzes the hydrolysis of glutamine to stoichiometric amounts of glutamate and ammonia. Originally thought to be liver-specific, this protein has been found in other tissues as well. Alternative splicing results in multiple transcript variants that encode different isoforms. [provided by RefSeq, Jul 2013]

Known Variants25 total

rsidPosition (GRCh37)AllelesClassClinVar
rs263831512:56,865,056G/Cupstream gene variant
rs265787912:56,865,338A/Tmissense variant
rs11570154812:56,865,339G/Auncertain significance
rs78127183612:56,865,620C/Tuncertain significance
rs263831412:56,866,334T/Aupstream gene variant
rs7876416712:56,867,013C/Tuncertain significance
rs75227115112:56,867,050G/Auncertain significance
rs254732182712:56,867,345C/Tuncertain significance
rs14592646012:56,868,451G/Alikely benign
rs77068919412:56,868,468C/Tuncertain significance
rs6173195812:56,868,666C/Tbenign
rs14141155012:56,868,851C/Tuncertain significance
rs76068922612:56,868,865C/Tuncertain significance
rs159227559912:56,869,405T/Clikely benign
rs56828001912:56,869,427T/Cuncertain significance
rs136363063512:56,869,439C/Tuncertain significance
rs254732723012:56,871,738T/Guncertain significance
rs254732723312:56,871,739G/Cuncertain significance
rs142760278212:56,871,797A/Cuncertain significance
rs254732730512:56,871,812A/Guncertain significance
rs77690045512:56,872,874G/Auncertain significance
rs78027588512:56,873,579C/Tuncertain significance
rs75228591312:56,874,097C/Tlikely benign
rs117089625212:56,874,154C/Tuncertain significance
rs187084231712:56,881,886G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.