KLHL8

kelch like family member 8

Summary

Predicted to enable ubiquitin-like ligase-substrate adaptor activity. Involved in protein ubiquitination and ubiquitin-dependent protein catabolic process. Located in nucleoplasm. Part of Cul3-RING ubiquitin ligase complex. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants27 total

rsidPosition (GRCh37)AllelesClassClinVar
rs17302755744:88,085,105T/Cuncertain significance
rs1403412514:88,085,177C/Tuncertain significance
rs2015022234:88,085,180C/Tuncertain significance
rs1440745044:88,085,192C/Tuncertain significance
rs3717185754:88,091,371C/Auncertain significance
rs12879810724:88,091,372C/Tuncertain significance
rs17305839514:88,091,389T/Cuncertain significance
rs11720612884:88,091,613A/Guncertain significance
rs14151258794:88,091,702G/Cuncertain significance
rs24765165964:88,091,703T/Auncertain significance
rs11882918144:88,097,997G/Auncertain significance
rs7651673744:88,099,644C/Auncertain significance
rs12652375384:88,099,684G/Cuncertain significance
rs24765338384:88,099,761A/Guncertain significance
rs1434050554:88,104,471T/Cuncertain significance
rs13217079414:88,104,486T/Cuncertain significance
rs7539725354:88,104,507A/Guncertain significance
rs9167663944:88,106,468C/Tuncertain significance
rs7592971814:88,106,609T/Cuncertain significance
rs1506327534:88,106,822C/Tuncertain significance
rs13746190014:88,106,851G/Auncertain significance
rs1421216184:88,116,591C/Auncertain significance
rs3730621094:88,116,684G/Auncertain significance
rs5654554654:88,135,875T/C
rs356243764:88,159,088T/Cintron variant
rs100292544:88,160,140C/G
rs119298744:88,162,100C/G

Gene information from NCBI Gene. Variant classifications from ClinVar.