LHPP

phospholysine phosphohistidine inorganic pyrophosphate phosphatase

Summary

Enables inorganic diphosphate phosphatase activity and protein homodimerization activity. Involved in phosphate-containing compound metabolic process. Located in cytosol and nuclear speck. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants47 total

rsidPosition (GRCh37)AllelesClassClinVar
rs14570938710:126,149,591A/Tupstream gene variant
rs37669796410:126,150,302T/G
rs76229541110:126,150,444G/Auncertain significance
rs129325560710:126,150,456G/Cuncertain significance
rs7542665210:126,150,523C/Amissense variant
rs125413977910:126,150,543G/Cuncertain significance
rs119644822810:126,150,544A/Guncertain significance
rs128138911210:126,150,547C/Tuncertain significance
rs14613457110:126,159,805C/Gregulatory region variant
rs6186192710:126,160,495G/T
rs75460166710:126,172,718T/Cuncertain significance
rs14546390010:126,172,722G/Auncertain significance
rs249474926110:126,172,739T/Cuncertain significance
rs20058324210:126,172,764G/Auncertain significance
rs37642164710:126,172,782A/Guncertain significance
rs94371216410:126,172,796G/Cuncertain significance
rs133108697710:126,172,886A/Tuncertain significance
rs11229980310:126,172,901A/Clikely benign
rs54529244710:126,172,954G/A
rs76136823510:126,176,997G/Auncertain significance
rs249477505010:126,177,045T/Cuncertain significance
rs20071074310:126,177,053G/Auncertain significance
rs146905573710:126,177,089G/Auncertain significance
rs77398725410:126,177,104A/Guncertain significance
rs77725981710:126,177,137G/Auncertain significance
rs56729426010:126,178,340T/A
rs53543728010:126,182,620C/T
rs19975489710:126,185,531C/Tuncertain significance
rs249482914710:126,185,561C/Guncertain significance
rs37545735210:126,186,641C/Auncertain significance
rs37607250210:126,186,647C/Tuncertain significance
rs76350513710:126,205,752G/Alikely benign
rs14082392810:126,205,767G/Abenign
rs53818759210:126,205,785G/Auncertain significance
rs20172750310:126,205,797C/Tuncertain significance
rs57301102810:126,205,816T/Guncertain significance
rs6173875410:126,205,829C/Tbenign
rs18873858310:126,223,051G/Aregulatory region variant
rs11222967410:126,242,184C/Gintron variant
rs3593651410:126,244,970C/Tintron variant
rs1090176910:126,264,311G/A
rs1277384610:126,275,914G/C
rs236250110:126,290,498G/Aintron variant
rs374054010:126,294,167G/Aintron variant
rs1224662310:126,294,395A/G
rs52847471610:126,301,843G/Auncertain significance
rs37679894710:126,301,853C/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.