MITF

melanocyte inducing transcription factor

Summary

The protein encoded by this gene is a transcription factor that contains both basic helix-loop-helix and leucine zipper structural features. The encoded protein regulates melanocyte development and is responsible for pigment cell-specific transcription of the melanogenesis enzyme genes. Heterozygous mutations in the this gene cause auditory-pigmentary syndromes, such as Waardenburg syndrome type 2 and Tietz syndrome. [provided by RefSeq, Aug 2017]

Known Variants605 total

rsidPosition (GRCh37)AllelesClassClinVar
rs76518913:69,788,321G/Abenign
rs7647237753:69,788,720C/Tlikely benign
rs7806425123:69,788,808G/Tuncertain significance
rs13230752943:69,788,812A/Guncertain significance
rs1432049333:69,788,920C/Glikely benign
rs455191353:69,789,096A/Clikely benign
rs729500373:69,812,844G/Tlikely benign
rs729500393:69,812,903C/Tbenign
rs9272403853:69,813,015C/Tlikely benign
rs14411018063:69,813,040C/Guncertain significance
rs13357737533:69,813,062A/Guncertain significance
rs7810879743:69,813,068T/Clikely benign
rs3736605473:69,813,078G/Aconflicting classifications of pathogenicity
rs5386741423:69,821,008C/T
rs783563563:69,824,093A/Gintron variant
rs605511653:69,827,409T/Cintron variant
rs622509763:69,835,405T/Gregulatory region variant
rs622509773:69,836,592G/Aregulatory region variant
rs21160003:69,838,613G/Aintron variant
rs130973793:69,842,428A/Gintron variant
rs1503217153:69,843,660T/Cuncertain significance
rs622509803:69,844,608G/Aintron variant
rs76267173:69,845,194A/Gintron variant
rs76368023:69,845,216G/A
rs622510093:69,849,835T/Cintron variant
rs14306093:69,854,587G/A
rs119171303:69,855,694T/Aintron variant
rs795023003:69,856,753C/A
rs76110203:69,856,827G/Aintron variant
rs622510273:69,862,454C/T
rs98364933:69,863,512T/Cintron variant
rs622510313:69,865,083T/A
rs15295843:69,870,760A/G
rs15295833:69,870,775G/T
rs11562553:69,878,088A/Cintron variant
rs68059243:69,879,670G/Tintron variant
rs67952493:69,879,741A/Tintron variant
rs68059453:69,879,759G/Aintron variant
rs176385383:69,880,673A/Tintron variant
rs604381833:69,880,729C/Tintron variant
rs622521823:69,881,433A/Gintron variant
rs622522163:69,881,906T/Cintron variant
rs749565893:69,886,006A/Gintron variant
rs622522393:69,893,971G/Tintron variant
rs622531773:69,906,267T/G
rs622531833:69,907,344C/Tintron variant
rs793750473:69,907,706C/Tintron variant
rs7793872743:69,915,449C/Tlikely benign
rs5678058243:69,915,453T/Clikely benign
rs2021666523:69,915,494A/Guncertain significance
rs7615979193:69,915,496C/Tuncertain significance
rs12261444433:69,928,245T/Clikely benign
rs12315873063:69,928,288T/Guncertain significance
rs14056598483:69,928,291C/Tlikely benign
rs3740972823:69,928,294C/Tlikely benign
rs1996974943:69,928,321G/Tlikely benign
rs14781305043:69,928,397C/Tuncertain significance
rs5425550953:69,928,426G/Alikely benign
rs7494319263:69,928,453C/Tlikely benign
rs3710805253:69,928,496C/Tconflicting classifications of pathogenicity
rs1902155883:69,928,509C/Tuncertain significance
rs98497763:69,928,510G/Abenign
rs7778446723:69,928,519G/Alikely benign
rs3704828583:69,928,525A/Glikely benign
rs7491858853:69,928,541G/Alikely benign
rs170065493:69,928,677G/Abenign
rs98330463:69,928,831A/Gbenign
rs98371373:69,928,861T/Cbenign
rs5611808323:69,945,379A/G
rs9956089753:69,985,754G/Auncertain significance
rs775889603:69,985,838G/Alikely benign
rs2014458193:69,985,846C/Tlikely benign
rs1995154693:69,985,860C/Tlikely benign
rs24715794473:69,985,870T/Alikely benign
rs7602736113:69,985,874A/Glikely pathogenic
rs14499641363:69,985,876G/Auncertain significance
rs7713163233:69,985,880G/Aconflicting classifications of pathogenicity
rs10281591593:69,985,890A/Guncertain significance
rs24715795553:69,985,892T/Cuncertain significance
rs24715795703:69,985,897T/Auncertain significance
rs24715795793:69,985,899A/Tuncertain significance
rs20658447543:69,985,900C/Guncertain significance
rs24715795923:69,985,901T/Auncertain significance
rs7770211503:69,985,902A/Guncertain significance
rs24715796113:69,985,904C/Tconflicting classifications of pathogenicity
rs15537014773:69,985,907G/Apathogenic
rs24715796533:69,985,908T/Cuncertain significance
rs12364365553:69,985,911G/Cpathogenic
rs7658384513:69,985,916A/Tlikely benign
rs21074744403:69,985,921G/Alikely benign
rs3691066783:69,985,923C/Alikely benign
rs3727011053:69,985,924T/Clikely benign
rs24715797313:69,985,925C/Tlikely benign
rs731173253:69,986,144G/Alikely benign
rs746770753:69,986,779A/Cbenign
rs24715845943:69,986,955C/Tlikely benign
rs14286657263:69,986,958C/Tlikely benign
rs8766578673:69,986,965A/Gconflicting classifications of pathogenicity
rs7760835193:69,986,966T/Clikely benign
rs15760045433:69,986,967G/Alikely benign

Showing 100 of 605 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.