NHERF2

NHERF family PDZ scaffold protein 2

Summary

This gene encodes a member of the NHERF family of PDZ scaffolding proteins. These proteins mediate many cellular processes by binding to and regulating the membrane expression and protein-protein interactions of membrane receptors and transport proteins. The encoded protein plays a role in intestinal sodium absorption by regulating the activity of the sodium/hydrogen exchanger 3, and may also regulate the cystic fibrosis transmembrane regulator (CFTR) ion channel. Alternatively spliced transcript variants encoding multiple isoforms have been observed for this gene. [provided by RefSeq, Nov 2011]

Known Variants47 total

rsidPosition (GRCh37)AllelesClassClinVar
rs208389024316:2,077,044G/Tuncertain significance
rs118540483716:2,077,060G/Tuncertain significance
rs97985172616:2,077,089A/Guncertain significance
rs7349608716:2,077,090G/Cbenign
rs99810143516:2,077,206A/Guncertain significance
rs55350798816:2,079,619C/Tuncertain significance
rs77185519616:2,079,620G/Auncertain significance
rs38790753916:2,079,621G/Auncertain significance
rs37086038216:2,079,682G/Auncertain significance
rs75472235816:2,079,698G/Auncertain significance
rs37392492516:2,079,712G/Cuncertain significance
rs36909724416:2,079,726G/Cuncertain significance
rs77464322416:2,079,731C/Tuncertain significance
rs77414999616:2,086,331A/Guncertain significance
rs36999117616:2,086,374G/Auncertain significance
rs38790754016:2,086,396G/Auncertain significance
rs13949178616:2,086,421C/Tlikely benign
rs55552630316:2,086,422G/Cuncertain significance
rs126023620916:2,086,438C/Guncertain significance
rs76049238816:2,086,440G/Auncertain significance
rs37499754316:2,086,452C/Tlikely benign
rs36768014316:2,086,466G/Auncertain significance
rs6203880016:2,086,469C/Tlikely benign
rs20086563416:2,086,481C/Guncertain significance
rs20032887716:2,086,484G/Auncertain significance
rs37162535916:2,086,493C/Tuncertain significance
rs77390889716:2,086,494G/Auncertain significance
rs76432328316:2,086,751G/Cuncertain significance
rs76742289216:2,086,756C/Tuncertain significance
rs37698221716:2,086,757G/Auncertain significance
rs5798662816:2,086,798G/Abenign
rs37173918316:2,086,805G/Auncertain significance
rs75246260816:2,086,846C/Tuncertain significance
rs4129227516:2,086,847G/Auncertain significance
rs20037479816:2,086,852C/Tuncertain significance
rs55859044616:2,086,853G/Auncertain significance
rs36835832616:2,086,867G/Auncertain significance
rs53613381816:2,086,965C/Tuncertain significance
rs75193226516:2,087,548G/Auncertain significance
rs87895818416:2,087,561C/Tuncertain significance
rs76341941816:2,087,585C/Tuncertain significance
rs36920622416:2,087,587G/Tuncertain significance
rs37712639916:2,087,885C/Tuncertain significance
rs20133847816:2,087,888C/Tuncertain significance
rs37190301416:2,087,893G/Auncertain significance
rs75146779716:2,087,921G/Auncertain significance
rs75015945416:2,087,963G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.