NSD1

nuclear receptor binding SET domain protein 1

Summary

This gene encodes a protein containing a SET domain, 2 LXXLL motifs, 3 nuclear translocation signals (NLSs), 4 plant homeodomain (PHD) finger regions, and a proline-rich region. The encoded protein enhances androgen receptor (AR) transactivation, and this enhancement can be increased further in the presence of other androgen receptor associated coregulators. This protein may act as a nucleus-localized, basic transcriptional factor and also as a bifunctional transcriptional regulator. Mutations of this gene have been associated with Sotos syndrome and Weaver syndrome. One version of childhood acute myeloid leukemia is the result of a cryptic translocation with the breakpoints occurring within nuclear receptor-binding Su-var, enhancer of zeste, and trithorax domain protein 1 on chromosome 5 and nucleoporin, 98-kd on chromosome 11. Multiple transcript variants encoding distinct isoforms have been identified for this gene. [provided by RefSeq, Sep 2018]

Known Variants1,344 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1415313745:176,558,056G/Aupstream gene variant
rs37338735:176,561,113T/Cbenign
rs1164196405:176,561,748C/Tlikely benign
rs738067305:176,561,982A/Glikely benign
rs1996392925:176,562,097G/Aconflicting classifications of pathogenicity
rs3683458465:176,562,123C/Aconflicting classifications of pathogenicity
rs7601609965:176,562,126C/Tlikely benign
rs17562037815:176,562,130G/Tconflicting classifications of pathogenicity
rs15810890745:176,562,133G/Auncertain significance
rs1434060175:176,562,138T/Cconflicting classifications of pathogenicity
rs13480593085:176,562,141C/Auncertain significance
rs15810891585:176,562,143G/Clikely benign
rs17562057615:176,562,146G/Clikely benign
rs17562072465:176,562,160C/Tuncertain significance
rs3773027415:176,562,162G/Tuncertain significance
rs1471467765:176,562,176C/Tconflicting classifications of pathogenicity
rs7523763085:176,562,181A/Glikely benign
rs9053202025:176,562,195C/Glikely benign
rs9238499955:176,562,201G/Auncertain significance
rs21497553435:176,562,209T/Guncertain significance
rs5490918735:176,562,212A/Guncertain significance
rs3685244945:176,562,217A/Glikely benign
rs15620976795:176,562,244C/Guncertain significance
rs24800862285:176,562,245T/Clikely benign
rs2007358775:176,562,246A/Gconflicting classifications of pathogenicity
rs13362736255:176,562,249C/Tuncertain significance
rs7786469375:176,562,255T/Clikely benign
rs7275040525:176,562,257G/Auncertain significance
rs24800864825:176,562,277A/Guncertain significance
rs10575239945:176,562,302A/Glikely benign
rs24800866755:176,562,303T/Auncertain significance
rs15620978495:176,562,311C/Apathogenic
rs7600290455:176,562,313T/Gconflicting classifications of pathogenicity
rs2017804075:176,562,326A/Glikely benign
rs7637813265:176,562,345A/Gconflicting classifications of pathogenicity
rs13421059535:176,562,346T/Cuncertain significance
rs8860425305:176,562,347G/Cuncertain significance
rs24800870595:176,562,356A/Glikely benign
rs12168487935:176,562,378G/Auncertain significance
rs2001936225:176,562,394T/Alikely benign
rs7798507425:176,562,397A/Tlikely benign
rs24800874925:176,562,423G/Auncertain significance
rs12017157875:176,562,435A/Glikely benign
rs17562318325:176,562,438G/Tuncertain significance
rs770939365:176,562,443C/Tlikely benign
rs7494449725:176,562,444A/Gconflicting classifications of pathogenicity
rs15810902825:176,562,450T/Guncertain significance
rs5877841025:176,562,456C/Glikely benign
rs21497558815:176,562,457C/Tuncertain significance
rs8860604385:176,562,480A/Guncertain significance
rs12121168815:176,562,485A/Tlikely benign
rs7646172655:176,562,487A/Guncertain significance
rs289321745:176,562,499G/Auncertain significance
rs10089860075:176,562,502A/Guncertain significance
rs24800882075:176,562,509C/Tlikely benign
rs9763372595:176,562,521G/Alikely benign
rs7458852595:176,562,540A/Glikely benign
rs12402590795:176,562,542C/Guncertain significance
rs9580201775:176,562,555C/Tlikely benign
rs7658451625:176,562,558C/Tlikely benign
rs794274335:176,562,584C/Tlikely benign
rs24800890235:176,562,586A/Tuncertain significance
rs5323459985:176,562,591G/Alikely benign
rs21497561745:176,562,594G/Auncertain significance
rs2010122285:176,562,611C/Tlikely benign
rs15541675485:176,562,628C/Tuncertain significance
rs17562515095:176,562,633G/Auncertain significance
rs5386189505:176,562,634A/Glikely benign
rs7585357705:176,562,653C/Tlikely benign
rs17562552405:176,562,661A/Tuncertain significance
rs7474828165:176,562,664C/Glikely benign
rs7691620625:176,562,671C/Tlikely benign
rs11861564135:176,562,673A/Tuncertain significance
rs14172369405:176,562,687T/Gconflicting classifications of pathogenicity
rs24800900995:176,562,689T/Clikely benign
rs15810914695:176,562,726G/Aconflicting classifications of pathogenicity
rs21497565025:176,562,730G/Auncertain significance
rs7559314585:176,562,743C/Tlikely benign
rs12089674705:176,562,745C/Tuncertain significance
rs7656127035:176,562,746A/Clikely benign
rs12401495225:176,562,757G/Tuncertain significance
rs7554490995:176,562,762G/Tuncertain significance
rs21497566485:176,562,765G/Tuncertain significance
rs10575244205:176,562,766C/Tuncertain significance
rs7701745125:176,562,774T/Cuncertain significance
rs13206225885:176,562,776G/Alikely benign
rs7705229995:176,562,786C/Gconflicting classifications of pathogenicity
rs10575223195:176,562,788A/Glikely benign
rs289321755:176,562,812G/Clikely benign
rs17562733265:176,562,813A/Guncertain significance
rs17562741695:176,562,821G/Alikely benign
rs11565105135:176,562,840G/Tlikely benign
rs7781288245:176,562,861C/Glikely benign
rs1493342445:176,562,864C/Tlikely benign
rs5583024215:176,562,871C/Tlikely benign
rs17562808685:176,562,873C/Tuncertain significance
rs3703286025:176,562,890C/Tlikely benign
rs7715872605:176,562,897A/Gconflicting classifications of pathogenicity
rs7667702975:176,562,908A/Glikely benign
rs7517874445:176,562,909G/Auncertain significance

Showing 100 of 1,344 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.