ORMDL3

ORMDL sphingolipid biosynthesis regulator 3

Summary

Involved in ceramide metabolic process. Acts upstream of or within several processes, including negative regulation of B cell apoptotic process; negative regulation of ceramide biosynthetic process; and positive regulation of protein localization to nucleus. Located in endoplasmic reticulum. Part of serine palmitoyltransferase complex. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants14 total

rsidPosition (GRCh37)AllelesClassClinVar
rs316957217:38,077,412G/Aupstream gene variant
rs197830533317:38,078,916T/Guncertain significance
rs76706977817:38,079,378T/Auncertain significance
rs76270107317:38,080,335G/Auncertain significance
rs120043058517:38,080,351C/Tuncertain significance
rs75878413717:38,080,383G/Auncertain significance
rs214474656817:38,080,384A/Guncertain significance
rs37486565017:38,080,396C/Tuncertain significance
rs76542718717:38,080,432C/Tuncertain significance
rs406527517:38,080,865A/T
rs807613117:38,080,912G/Aregulatory region variant
rs1260333217:38,082,807T/Cregulatory region variant
rs1760892517:38,082,831T/Cregulatory region variant
rs374424617:38,084,350T/A

Gene information from NCBI Gene. Variant classifications from ClinVar.