PALS2

protein associated with LIN7 2, MAGUK p55 family member

Summary

Members of the peripheral membrane-associated guanylate kinase (MAGUK) family function in tumor suppression and receptor clustering by forming multiprotein complexes containing distinct sets of transmembrane, cytoskeletal, and cytoplasmic signaling proteins. All MAGUKs contain a PDZ-SH3-GUK core and are divided into 4 subfamilies, DLG-like (see DLG1; MIM 601014), ZO1-like (see TJP1; MIM 601009), p55-like (see MPP1; MIM 305360), and LIN2-like (see CASK; MIM 300172), based on their size and the presence of additional domains. MPP6 is a member of the p55-like MAGUK subfamily (Tseng et al., 2001 [PubMed 11311936]).[supplied by OMIM, Mar 2008]

Known Variants26 total

rsidPosition (GRCh37)AllelesClassClinVar
rs25290907:24,662,280C/Gintron variant
rs7712833487:24,663,347G/Auncertain significance
rs5756275037:24,681,294C/Aintron variant
rs25347289807:24,681,368G/Cuncertain significance
rs8901404137:24,689,264A/Guncertain significance
rs11673168227:24,689,295A/Guncertain significance
rs25347707837:24,690,128A/Cuncertain significance
rs7644291097:24,690,167A/Guncertain significance
rs7520931737:24,690,174G/Auncertain significance
rs12899348817:24,690,201T/Auncertain significance
rs3688968937:24,690,216A/Guncertain significance
rs171497737:24,690,277A/Gbenign
rs7602375737:24,690,279G/Auncertain significance
rs27218007:24,692,552G/T
rs7679117447:24,703,215G/Tuncertain significance
rs1999278557:24,703,307G/Tuncertain significance
rs25348292207:24,705,289G/Auncertain significance
rs3756344177:24,708,272G/Alikely benign
rs792109637:24,717,969T/Cupstream gene variant
rs17877873297:24,718,830A/Guncertain significance
rs17877918197:24,718,899A/Guncertain significance
rs171498567:24,720,073G/Abenign
rs7705120277:24,720,078A/Guncertain significance
rs3763704717:24,720,087G/Auncertain significance
rs11593490667:24,727,113C/Auncertain significance
rs7499725217:24,727,201C/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.