PCDHA9

protocadherin alpha 9

Summary

This gene is a member of the protocadherin alpha gene cluster, one of three related gene clusters tandemly linked on chromosome five that demonstrate an unusual genomic organization similar to that of B-cell and T-cell receptor gene clusters. The alpha gene cluster is composed of 15 cadherin superfamily genes related to the mouse CNR genes and consists of 13 highly similar and 2 more distantly related coding sequences. The tandem array of 15 N-terminal exons, or variable exons, are followed by downstream C-terminal exons, or constant exons, which are shared by all genes in the cluster. The large, uninterrupted N-terminal exons each encode six cadherin ectodomains while the C-terminal exons encode the cytoplasmic domain. These neural cadherin-like cell adhesion proteins are integral plasma membrane proteins that most likely play a critical role in the establishment and function of specific cell-cell connections in the brain. Alternative splicing has been observed and additional variants have been suggested but their full-length nature has yet to be determined. [provided by RefSeq, Jul 2008]

Known Variants120 total

rsidPosition (GRCh37)AllelesClassClinVar
rs17815776045:140,228,111G/Tuncertain significance
rs2513535:140,228,164A/Clikely benign
rs1479066095:140,228,194A/Glikely benign
rs1416400035:140,228,197C/Tlikely benign
rs1470996295:140,228,198G/Alikely benign
rs1382584105:140,228,203C/Tlikely benign
rs1492270215:140,228,205G/Auncertain significance
rs1867805435:140,228,208C/Auncertain significance
rs7819282305:140,228,243G/Cuncertain significance
rs11738709105:140,228,252G/Cuncertain significance
rs7819382035:140,228,265G/Tuncertain significance
rs569264515:140,228,272C/Glikely benign
rs7819059255:140,228,291C/Tuncertain significance
rs7817860655:140,228,358A/Tuncertain significance
rs1462536285:140,228,366T/Glikely benign
rs13177611945:140,228,379C/Tuncertain significance
rs178443225:140,228,410A/Glikely benign
rs178443235:140,228,413C/Alikely benign
rs3699030735:140,228,417C/Guncertain significance
rs3739125545:140,228,446G/Alikely benign
rs7824332705:140,228,464C/Guncertain significance
rs3640635:140,228,473A/Glikely benign
rs12233395395:140,228,484C/Auncertain significance
rs7818018905:140,228,518G/Alikely benign
rs5390514465:140,228,525G/Auncertain significance
rs2013051865:140,228,532G/Tuncertain significance
rs7819093135:140,228,577C/Tuncertain significance
rs20407496285:140,228,613T/Guncertain significance
rs15541427835:140,228,748C/Tuncertain significance
rs12747159705:140,228,780G/Auncertain significance
rs7825901185:140,228,870C/Guncertain significance
rs3754752845:140,228,896C/Tlikely benign
rs15541428825:140,228,907A/Cuncertain significance
rs7818506095:140,229,024C/Auncertain significance
rs2019452185:140,229,029A/Cuncertain significance
rs15541429815:140,229,081G/Auncertain significance
rs2513545:140,229,086C/Glikely benign
rs5688533805:140,229,132C/Tlikely benign
rs7723028165:140,229,155G/Cuncertain significance
rs7818644265:140,229,174T/Cuncertain significance
rs7819021145:140,229,182G/Tuncertain significance
rs1401389485:140,229,235T/Gbenign
rs1389488675:140,229,259C/Tlikely benign
rs3719365385:140,229,278A/Cuncertain significance
rs25476353055:140,229,285A/Guncertain significance
rs7827682695:140,229,297C/Tuncertain significance
rs1414950635:140,229,302G/Cuncertain significance
rs77229275:140,229,316T/Cbenign
rs15541432455:140,229,328G/Cuncertain significance
rs2513555:140,229,368C/Glikely benign
rs7818293075:140,229,369G/Auncertain significance
rs5663722585:140,229,382A/Glikely benign
rs5537503655:140,229,400G/Clikely benign
rs1453338135:140,229,417C/Guncertain significance
rs7826539165:140,229,422G/Auncertain significance
rs3697461555:140,229,428G/Auncertain significance
rs1487326915:140,229,436A/Tbenign
rs14515855915:140,229,445C/Tlikely benign
rs7827333465:140,229,450A/Guncertain significance
rs7818772045:140,229,452T/Clikely benign
rs5582188175:140,229,463G/Alikely benign
rs1512994605:140,229,499C/Tlikely benign
rs5444602285:140,229,518C/Tuncertain significance
rs25476422205:140,229,524G/Tuncertain significance
rs2513565:140,229,526T/Glikely benign
rs13643550405:140,229,529C/Auncertain significance
rs7819917295:140,229,557T/Cuncertain significance
rs7824812695:140,229,570G/Tuncertain significance
rs7825857865:140,229,575T/Glikely benign
rs590560235:140,229,581G/Cbenign
rs7820175815:140,229,588C/Tuncertain significance
rs8799711505:140,229,591T/Auncertain significance
rs14150631375:140,229,597G/Auncertain significance
rs5339876035:140,229,623G/Auncertain significance
rs1397196265:140,229,680C/Tlikely benign
rs7825503695:140,229,688C/Auncertain significance
rs5778009255:140,229,694C/Glikely benign
rs5451928155:140,229,695G/Auncertain significance
rs5273990655:140,229,708C/Guncertain significance
rs7827093965:140,229,729C/Tuncertain significance
rs178443335:140,229,794G/Clikely benign
rs7674626005:140,229,795G/Auncertain significance
rs14116398825:140,229,797A/Cuncertain significance
rs5695333865:140,229,814C/Guncertain significance
rs3713053255:140,229,845G/Tuncertain significance
rs15541441465:140,229,878G/Auncertain significance
rs7824759855:140,229,900T/Guncertain significance
rs1397170335:140,229,914C/Alikely benign
rs587920005:140,229,925G/Clikely benign
rs1467271405:140,229,926G/Tuncertain significance
rs7821198275:140,229,931C/Auncertain significance
rs3734543785:140,229,987C/Tlikely benign
rs3691268965:140,229,995G/Cuncertain significance
rs7823790395:140,230,001G/Auncertain significance
rs1997851835:140,230,017G/Tuncertain significance
rs7821436755:140,230,095G/Cuncertain significance
rs1152187495:140,230,122G/Alikely benign
rs15541444905:140,230,126G/Tlikely benign
rs1120461005:140,230,137C/Alikely benign
rs7818897475:140,230,164A/Guncertain significance

Showing 100 of 120 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.