PON3

paraoxonase 3

Summary

This gene is a member of the paraoxonase family and lies in a cluster on chromosome 7 with the other two family members. The encoded protein is secreted into the bloodstream and associates with high-density lipoprotein (HDL). The protein also rapidly hydrolyzes lactones and can inhibit the oxidation of low-density lipoprotein (LDL), a function that is believed to slow the initiation and progression of atherosclerosis. Alternatively spliced variants which encode different protein isoforms have been described; however, only one has been fully characterized. [provided by RefSeq, Jul 2008]

Known Variants61 total

rsidPosition (GRCh37)AllelesClassClinVar
rs2017453037:94,989,318G/Abenign
rs1398565357:94,989,379C/Tbenign
rs3741359027:94,989,411C/Guncertain significance
rs2016616767:94,989,434T/Auncertain significance
rs12060942197:94,989,437G/Auncertain significance
rs3769068167:94,989,448C/Tlikely benign
rs20743527:94,989,673C/Tbenign
rs178840007:94,991,632T/Cbenign
rs5628029677:94,991,729T/Auncertain significance
rs1452457807:94,991,764G/Alikely benign
rs1386671277:94,992,064A/Gbenign
rs7676473727:94,992,076A/Tuncertain significance
rs1426208257:94,992,109A/Guncertain significance
rs109531437:94,992,244T/Cbenign
rs20743537:94,992,908G/Abenign
rs18086325867:94,993,178T/Cuncertain significance
rs7510099297:94,993,194T/Cuncertain significance
rs178804707:94,993,261A/Glikely benign
rs7635620117:94,993,314T/Auncertain significance
rs178830137:94,993,334G/Tbenign
rs2015445667:94,993,374C/Tuncertain significance
rs1928202087:94,994,064C/Tintron variant
rs1475953107:94,995,226G/Cintron variant
rs7712694677:94,996,726G/Tuncertain significance
rs7747662767:94,996,727T/Auncertain significance
rs178788277:94,996,732C/Tbenign
rs1413507407:94,996,741A/Gbenign
rs1379884957:94,996,760C/Auncertain significance
rs24948437007:94,996,762T/Cuncertain significance
rs7649970027:94,996,780C/Tuncertain significance
rs37577087:94,996,913T/Gbenign
rs1921580827:94,999,190G/Cintron variant
rs23750027:95,001,358T/Abenign
rs13149599257:95,001,545T/Guncertain significance
rs10532757:95,001,555C/Tbenign
rs5615701157:95,001,585A/Cuncertain significance
rs3773903997:95,001,618C/Alikely benign
rs5658695997:95,002,120T/C
rs5781411337:95,003,741C/T
rs5456462817:95,006,256G/A
rs1840369627:95,012,768A/Cintron variant
rs69773897:95,019,355G/Abenign
rs5663364947:95,019,489T/Cuncertain significance
rs7493825487:95,019,512G/Auncertain significance
rs104871327:95,020,305A/Gintron variant
rs7402647:95,021,803T/Gintron variant
rs1466437597:95,022,649A/Gintron variant
rs1838924297:95,023,483A/Tintron variant
rs1459035967:95,023,794G/Cintron variant
rs12104234647:95,023,994G/Auncertain significance
rs1470066957:95,024,007G/Aconflicting classifications of pathogenicity
rs1397902277:95,024,017C/Tlikely benign
rs119709107:95,024,046A/Gbenign
rs20721997:95,025,453A/Gbenign
rs7525522197:95,025,593A/Tuncertain significance
rs132261497:95,025,600G/Asynonymous variantbenign
rs1466279527:95,025,658C/Tlikely benign
rs178825397:95,026,408G/Aupstream gene variant
rs117677877:95,026,753T/Cupstream gene variant
rs1835733387:95,027,278T/Cupstream gene variant
rs1874441037:95,027,430A/Gupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.