SEC23IP

SEC23 interacting protein

Summary

This gene encodes a member of the phosphatidic acid preferring-phospholipase A1 family. The encoded protein is localized to endoplasmic reticulum exit sites and plays a critical role in ER-Golgi transport as part of the multimeric coat protein II complex. An orthologous gene in frogs is required for normal neural crest cell development, suggesting that this gene may play a role in Waardenburg syndrome neural crest defects. Alternatively spliced transcript variants have been observed for this gene. [provided by RefSeq, Feb 2011]

Known Variants80 total

rsidPosition (GRCh37)AllelesClassClinVar
rs77089357310:121,652,304A/Guncertain significance
rs146675085810:121,652,317G/Cuncertain significance
rs77430033610:121,652,374C/Tuncertain significance
rs249359973410:121,652,380C/Tuncertain significance
rs14353368810:121,652,395A/Guncertain significance
rs7335783310:121,652,427G/Abenign
rs14113225110:121,652,442C/Tbenign
rs75082411410:121,657,999C/Tuncertain significance
rs709409810:121,658,105A/Gbenign
rs18752519910:121,658,117C/Tlikely benign
rs249361417410:121,658,118A/Guncertain significance
rs74561752510:121,658,188C/Tuncertain significance
rs76826315910:121,658,198A/Tuncertain significance
rs75425968010:121,658,223A/Guncertain significance
rs75460311110:121,658,288A/Tuncertain significance
rs14599704310:121,658,325C/Tuncertain significance
rs20146438610:121,658,365C/Tuncertain significance
rs14895536610:121,658,400T/Cbenign
rs20144861110:121,658,454C/Guncertain significance
rs75672840010:121,658,467C/Guncertain significance
rs74634378210:121,658,470C/Tuncertain significance
rs245672210:121,659,811A/T
rs1119911610:121,660,400A/Cintron variant
rs91606845610:121,662,353G/Tuncertain significance
rs14710254610:121,662,413G/Auncertain significance
rs249362349110:121,662,422C/Tuncertain significance
rs249362368810:121,662,514T/Auncertain significance
rs11494195510:121,663,619G/Auncertain significance
rs141303456010:121,663,665G/Auncertain significance
rs249362630310:121,663,673A/Cuncertain significance
rs36800697210:121,668,546A/Clikely benign
rs14039345510:121,668,548T/Abenign
rs20043364810:121,671,601A/Glikely benign
rs14266585410:121,671,605C/Tlikely benign
rs139307814010:121,671,633T/Alikely benign
rs1709936810:121,671,651T/Cbenign
rs121638592610:121,671,679G/Alikely benign
rs14978504210:121,674,292C/Tuncertain significance
rs20190564110:121,675,251C/Abenign
rs14567961810:121,675,324C/Tlikely benign
rs14773823010:121,675,376G/Auncertain significance
rs133798867010:121,675,392G/Auncertain significance
rs75754140010:121,677,380G/Tuncertain significance
rs75051475610:121,677,383G/Auncertain significance
rs77470265810:121,677,457G/Auncertain significance
rs120548001310:121,677,987T/Clikely benign
rs7972886510:121,678,590C/Tintron variant
rs36946567710:121,678,957T/Cuncertain significance
rs128893093310:121,678,959C/Auncertain significance
rs11404552710:121,678,995G/Cbenign
rs247529810:121,679,013A/Gbenign
rs249366207910:121,679,101A/Guncertain significance
rs1119912110:121,679,833C/Aintron variant
rs14497393010:121,683,274T/Cintron variant
rs1277187310:121,685,559G/Abenign
rs15019208410:121,685,579C/Tlikely benign
rs14147425410:121,685,653A/Guncertain significance
rs20216460010:121,685,654A/Guncertain significance
rs76015123910:121,685,734G/Auncertain significance
rs14061557810:121,685,749C/Tbenign
rs5612277810:121,687,731T/Gintron variant
rs14533878810:121,689,182A/Cuncertain significance
rs14775433910:121,689,188A/Guncertain significance
rs13997741510:121,689,232C/Tlikely benign
rs19060669410:121,689,273C/Tuncertain significance
rs20063373210:121,689,855A/Glikely benign
rs78151969510:121,691,741G/Auncertain significance
rs78006696610:121,691,749A/Guncertain significance
rs36925514210:121,691,805A/Tuncertain significance
rs77763788710:121,692,537C/Tuncertain significance
rs14897018410:121,692,565T/Cuncertain significance
rs249369158010:121,692,582T/Auncertain significance
rs76248028710:121,692,600A/Guncertain significance
rs5811148110:121,693,194A/Tbenign
rs37738037710:121,693,242G/Auncertain significance
rs3482696410:121,693,246A/Gbenign
rs37537051010:121,693,250A/Guncertain significance
rs14459435410:121,693,276T/Clikely benign
rs7282646610:121,695,483A/Gintron variant
rs1068610:121,701,160G/T3 prime UTR variant

Gene information from NCBI Gene. Variant classifications from ClinVar.