SEZ6

seizure related 6 homolog

Summary

The protein encoded by this gene is thought to contain five cysteine-rich motifs that are similar to sushi domains, as well as two domains similar to the amino terminal half of the CUB (for complement C1r/C1s, Uegf, Bmp1) domain. Mutations in this gene have been associated with febrile seizures. [provided by RefSeq, Jul 2016]

Known Variants60 total

rsidPosition (GRCh37)AllelesClassClinVar
rs76449461517:27,283,214A/Guncertain significance
rs20120442817:27,283,236G/Auncertain significance
rs77079154017:27,283,247C/Tuncertain significance
rs19995500317:27,283,248G/Auncertain significance
rs20088113617:27,283,450C/Tuncertain significance
rs134828824917:27,283,456G/Cuncertain significance
rs14833659817:27,283,752T/Clikely benign
rs77698553717:27,284,094A/Gbenign
rs6173797417:27,284,194T/Cbenign
rs37657256817:27,284,209C/Tlikely benign
rs77839960917:27,284,368A/Cuncertain significance
rs1294188417:27,284,443G/Abenign
rs20139012017:27,284,503C/Tuncertain significance
rs116425341817:27,284,518C/Tuncertain significance
rs137902291917:27,284,984G/Tuncertain significance
rs37494731817:27,285,002G/Cuncertain significance
rs77868597717:27,285,135G/Auncertain significance
rs75829253917:27,285,150C/Tuncertain significance
rs37583920017:27,285,151G/Auncertain significance
rs74934956317:27,286,058C/Tuncertain significance
rs11481387617:27,286,153C/Tbenign
rs55725812517:27,286,355C/Tuncertain significance
rs20120686717:27,286,422C/Tbenign
rs6173797217:27,286,462C/Tbenign
rs20182179517:27,286,753G/Clikely benign
rs138425000317:27,286,773T/Cuncertain significance
rs54307269817:27,286,809C/Tuncertain significance
rs147071374717:27,287,615A/Guncertain significance
rs77764147617:27,287,947C/Tuncertain significance
rs254530641917:27,287,949A/Guncertain significance
rs76982362617:27,287,965C/Tuncertain significance
rs55270218517:27,287,970C/Tuncertain significance
rs20045977817:27,290,989C/Tbenign
rs6173797717:27,291,046C/Tbenign
rs76930337917:27,291,081C/Tuncertain significance
rs129347909717:27,296,825T/Cuncertain significance
rs77635833617:27,296,873C/Tuncertain significance
rs76818862117:27,296,897A/Cuncertain significance
rs74651949417:27,296,918C/Auncertain significance
rs132910196817:27,296,939G/Auncertain significance
rs37482031717:27,296,951C/Tlikely benign
rs56891249117:27,298,292A/C
rs74958852917:27,306,770G/Alikely benign
rs77795182617:27,308,427G/Cuncertain significance
rs254534652817:27,308,457C/Tuncertain significance
rs6173853917:27,308,503C/Tbenign
rs74853393417:27,308,541A/Guncertain significance
rs19955726517:27,308,629C/Tuncertain significance
rs20075806817:27,308,767G/Auncertain significance
rs36946078617:27,308,793A/Cuncertain significance
rs254534889717:27,308,887A/Cuncertain significance
rs124342889217:27,308,932C/Auncertain significance
rs18909056517:27,308,955C/Tuncertain significance
rs18103107617:27,308,971G/Tlikely benign
rs254534926517:27,308,995C/Tuncertain significance
rs20143558217:27,309,034C/Tlikely benign
rs86768326317:27,309,046C/Tuncertain significance
rs989155317:27,313,287T/Cregulatory region variant
rs3403948817:27,320,232G/Aintron variant
rs14691037717:27,326,611C/Tintron variant

Gene information from NCBI Gene. Variant classifications from ClinVar.