SPI1

Spi-1 proto-oncogene

Summary

This gene encodes an ETS-domain transcription factor that activates gene expression during myeloid and B-lymphoid cell development. The nuclear protein binds to a purine-rich sequence known as the PU-box found near the promoters of target genes, and regulates their expression in coordination with other transcription factors and cofactors. The protein can also regulate alternative splicing of target genes. Multiple transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2008]

Known Variants42 total

rsidPosition (GRCh37)AllelesClassClinVar
rs105723311:47,376,448G/Aregulatory region variant
rs20168560611:47,376,831C/Tuncertain significance
rs209590640411:47,376,869A/Clikely pathogenic
rs76506498011:47,376,902C/Gconflicting classifications of pathogenicity
rs209590654711:47,376,959T/Glikely pathogenic
rs249579587411:47,377,018C/Tlikely pathogenic
rs7147590911:47,377,283A/C
rs1076925611:47,378,396C/G
rs154232111:47,379,615G/C
rs1073455711:47,380,061A/Cbenign
rs54450140111:47,380,142A/G
rs374068811:47,380,340G/Tintron variantbenign
rs55850379611:47,380,446C/Tuncertain significance
rs75721050011:47,380,479C/Tuncertain significance
rs249581078411:47,380,500T/Auncertain significance
rs209591657411:47,380,525G/Cpathogenic
rs374068911:47,380,593A/Gbenign
rs214288439311:47,381,406G/Apathogenic
rs159585740611:47,381,423T/Guncertain significance
rs13893456911:47,381,441G/Auncertain significance
rs75637578111:47,381,451C/Tuncertain significance
rs36821528111:47,381,548G/Alikely benign
rs249581372711:47,381,593T/Gpathogenic
rs710585111:47,383,275T/Cintron variant
rs14194788011:47,385,350C/Tintron variant
rs1280118811:47,388,214G/Aregulatory region variant
rs3599635011:47,389,223A/Gregulatory region variant
rs475298711:47,390,692A/Gintron variant
rs1076925811:47,391,039C/A
rs475282911:47,396,654G/Aintron variant
rs249584256711:47,397,229G/Auncertain significance
rs5603082411:47,397,353G/Abenign
rs1214656511:47,398,963G/Aregulatory region variant
rs77155552211:47,399,862G/Cbenign
rs711195711:47,409,212C/Tupstream gene variant
rs1182191711:47,410,166T/C
rs1280352511:47,413,475G/Aintron variant
rs14575800311:47,414,372G/Aintron variant
rs1280227311:47,418,306T/Cupstream gene variant
rs5896562211:47,418,465C/Gupstream gene variant
rs87489611:47,418,953C/T
rs792448511:47,419,129A/T

Gene information from NCBI Gene. Variant classifications from ClinVar.