SPPL3

signal peptide peptidase like 3

Summary

Enables aspartic endopeptidase activity, intramembrane cleaving and protein homodimerization activity. Involved in T cell receptor signaling pathway; membrane protein proteolysis; and positive regulation of calcineurin-NFAT signaling cascade. Located in Golgi-associated vesicle membrane; endoplasmic reticulum; and plasma membrane. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants36 total

rsidPosition (GRCh37)AllelesClassClinVar
rs649030312:121,202,952A/C
rs76147488312:121,205,356T/Cuncertain significance
rs15088291112:121,206,182T/Cuncertain significance
rs249995992612:121,206,185G/Tuncertain significance
rs249995997712:121,206,219G/Cuncertain significance
rs239371712:121,220,375G/A
rs67983312:121,220,820A/C
rs77396677212:121,222,289T/Cuncertain significance
rs14245100712:121,222,355T/Cuncertain significance
rs58400112:121,228,055G/C
rs70878512:121,228,791G/C
rs7720523212:121,231,816A/Cintron variant
rs103930212:121,236,258C/G
rs13821372112:121,238,607C/Tregulatory region variant
rs14454715212:121,240,214G/T
rs54564702612:121,240,248T/G
rs14391145312:121,248,687G/Auncertain significance
rs56412012:121,250,932T/G
rs18607080412:121,263,788A/C
rs1282574612:121,268,033A/Cregulatory region variant
rs53270312:121,273,143C/Gintron variant
rs14915691012:121,273,195A/Gintron variant
rs57201612:121,279,083G/Adownstream gene variant
rs246147512:121,290,174T/Cintron variant
rs246147612:121,290,250T/A
rs60970012:121,297,487A/Gintron variant
rs66054912:121,300,988T/Cintron variant
rs11357304512:121,305,463G/T
rs14134642912:121,306,178C/Tintron variant
rs65693312:121,316,252A/T
rs5975790812:121,319,417T/Cintron variant
rs270117412:121,325,895T/Cintron variant
rs18715078712:121,327,809G/Aintron variant
rs116894812:121,330,365C/G
rs1106531812:121,334,133C/Aintron variant
rs239371612:121,341,933C/Gregulatory region variant

Gene information from NCBI Gene. Variant classifications from ClinVar.