SYNE3

spectrin repeat containing nuclear envelope family member 3

Summary

Enables actin filament binding activity and cytoskeleton-nuclear membrane anchor activity. Involved in cytoskeleton organization; establishment of protein localization to membrane; and regulation of cell shape. Located in nuclear membrane. Part of meiotic nuclear membrane microtubule tethering complex. Biomarker of Huntington's disease. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants88 total

rsidPosition (GRCh37)AllelesClassClinVar
rs36857404014:95,884,200G/Auncertain significance
rs14636834314:95,884,209C/Tuncertain significance
rs15075211614:95,884,225C/Auncertain significance
rs133183378014:95,884,236C/Tuncertain significance
rs74626294214:95,884,330G/Auncertain significance
rs1289538914:95,892,274G/Aintron variant
rs37550310714:95,898,432G/Auncertain significance
rs76427319514:95,898,433G/Auncertain significance
rs56952953214:95,899,647A/Guncertain significance
rs131191714314:95,899,663C/Auncertain significance
rs37075623614:95,899,686G/Auncertain significance
rs76980444714:95,899,713G/Cuncertain significance
rs54203350614:95,899,734G/Auncertain significance
rs188611152714:95,903,191G/Auncertain significance
rs76451103914:95,903,302T/Cuncertain significance
rs14640779114:95,905,377C/Tuncertain significance
rs77955206714:95,905,397C/Tuncertain significance
rs134650528614:95,905,453T/Guncertain significance
rs76521205814:95,905,458G/Auncertain significance
rs75903394814:95,905,486A/Cuncertain significance
rs250373408414:95,905,995C/Auncertain significance
rs250373419714:95,906,015T/Guncertain significance
rs57247880814:95,906,022C/Tuncertain significance
rs74833722414:95,906,024G/Auncertain significance
rs37164769614:95,906,102G/Auncertain significance
rs74957739014:95,906,259C/Tuncertain significance
rs213939274514:95,906,264T/Cuncertain significance
rs75663917914:95,906,301G/Auncertain significance
rs18841856414:95,906,374G/Cuncertain significance
rs76700322514:95,906,394G/Auncertain significance
rs77164999714:95,909,541T/Cuncertain significance
rs37295393514:95,909,576C/Auncertain significance
rs20084033614:95,909,607A/Tuncertain significance
rs75047286014:95,909,616T/Cuncertain significance
rs56560839714:95,910,934G/Auncertain significance
rs77260195014:95,910,965T/Cuncertain significance
rs55681816614:95,912,258T/Guncertain significance
rs14717842814:95,912,322A/Cuncertain significance
rs92179560814:95,912,326G/Auncertain significance
rs76494500014:95,912,331G/Alikely benign
rs76969075814:95,912,407G/Auncertain significance
rs14734541714:95,912,414T/Auncertain significance
rs75414296614:95,916,313G/Cuncertain significance
rs75284125614:95,916,336G/Cuncertain significance
rs141966248714:95,916,341G/Tuncertain significance
rs91345874814:95,916,344A/Cuncertain significance
rs75606143414:95,916,377C/Tuncertain significance
rs53145724514:95,918,635T/Cuncertain significance
rs14653271814:95,918,677C/Tuncertain significance
rs14922029314:95,918,678G/Auncertain significance
rs14341436814:95,918,687G/Auncertain significance
rs74976882614:95,918,714G/Auncertain significance
rs77097561614:95,921,730T/Clikely benign
rs77671545114:95,921,732T/Clikely benign
rs77118413214:95,921,733G/Tuncertain significance
rs78120801714:95,921,734C/Tuncertain significance
rs37546730414:95,921,743C/Tuncertain significance
rs77818750314:95,921,757G/Auncertain significance
rs77060761314:95,921,880C/Tlikely benign
rs19949778214:95,921,887G/Auncertain significance
rs56709680614:95,921,911C/Tuncertain significance
rs20000183114:95,921,965C/Tuncertain significance
rs14868705914:95,921,988C/Tlikely benign
rs37654703114:95,923,530C/Tuncertain significance
rs20218357314:95,923,557C/Tuncertain significance
rs19988336914:95,923,625C/Guncertain significance
rs76378528914:95,923,671C/Tuncertain significance
rs75118343414:95,923,672G/Auncertain significance
rs76845571214:95,932,324C/Tuncertain significance
rs136724717114:95,932,476A/Tuncertain significance
rs76777225314:95,932,516G/Auncertain significance
rs144404602514:95,932,521A/Guncertain significance
rs20141875914:95,934,192C/Tlikely benign
rs14800258014:95,934,253G/Auncertain significance
rs77009132214:95,934,270C/Tlikely benign
rs37677907014:95,934,283C/Tuncertain significance
rs135427562314:95,934,297C/Tuncertain significance
rs77652974414:95,942,017C/Tuncertain significance
rs124514719914:95,942,035C/Tuncertain significance
rs75669849414:95,942,043G/Auncertain significance
rs37024422214:95,942,058T/Cuncertain significance
rs99363151214:95,942,104A/Guncertain significance
rs20030913014:95,942,112G/Auncertain significance
rs75856326714:95,942,145G/Auncertain significance
rs1162288714:95,942,447A/Cupstream gene variant
rs73431314:95,956,572G/Cintergenic variant
rs17915114:95,981,829G/C
rs17914614:95,983,898A/Tregulatory region variant

Gene information from NCBI Gene. Variant classifications from ClinVar.