ABCB4

ATP binding cassette subfamily B member 4

Summary

The membrane-associated protein encoded by this gene is a member of the superfamily of ATP-binding cassette (ABC) transporters. ABC proteins transport various molecules across extra- and intra-cellular membranes. ABC genes are divided into seven distinct subfamilies (ABC1, MDR/TAP, MRP, ALD, OABP, GCN20, White). This protein is a member of the MDR/TAP subfamily. Members of the MDR/TAP subfamily are involved in multidrug resistance as well as antigen presentation. This gene encodes a full transporter and member of the p-glycoprotein family of membrane proteins with phosphatidylcholine as its substrate. The function of this protein has not yet been determined; however, it may involve transport of phospholipids from liver hepatocytes into bile. Alternative splicing of this gene results in several products of undetermined function. [provided by RefSeq, Jul 2008]

Known Variants792 total

rsidPosition (GRCh37)AllelesClassClinVar
rs774633677:87,006,034C/Gintron variant
rs1474230007:87,013,106C/Tintron variant
rs77768677:87,014,355C/Tintron variant
rs1177885957:87,021,524G/Aintron variant
rs288602897:87,024,685A/C
rs1150386987:87,024,718C/A
rs1446567117:87,025,346T/Aintron variant
rs7547709117:87,031,414A/Tlikely pathogenic
rs10293500227:87,031,436G/Aconflicting classifications of pathogenicity
rs7682364697:87,031,441T/Guncertain significance
rs11761455767:87,031,487C/Tlikely benign
rs1475770357:87,031,488G/Auncertain significance
rs18078317407:87,031,501T/Guncertain significance
rs7529130747:87,031,508C/Tlikely benign
rs25467357137:87,031,515T/Guncertain significance
rs25467357257:87,031,520C/Alikely benign
rs7722069417:87,031,547G/Aconflicting classifications of pathogenicity
rs11607110867:87,031,557C/Tuncertain significance
rs3691479997:87,031,558G/Auncertain significance
rs21162959307:87,031,560T/Cuncertain significance
rs7684486867:87,031,572A/Cuncertain significance
rs7693063137:87,031,576A/Cuncertain significance
rs1447909687:87,031,581C/Tuncertain significance
rs7520809587:87,031,588C/Tuncertain significance
rs21162964797:87,031,593G/Tuncertain significance
rs25467359947:87,031,601C/Tlikely benign
rs11804291507:87,031,609C/Tuncertain significance
rs2004040417:87,031,610T/Clikely benign
rs455496417:87,031,690A/Gbenign
rs15260907:87,031,809A/Gbenign
rs456139417:87,031,846T/Gbenign
rs454372957:87,032,251G/Tbenign
rs455520367:87,032,367T/Clikely benign
rs14836707777:87,032,432G/Alikely benign
rs18079242567:87,032,435G/Tlikely benign
rs12206887367:87,032,441C/Tlikely benign
rs15543969177:87,032,442C/Tconflicting classifications of pathogenicity
rs12454729047:87,032,450C/Apathogenic
rs14774488077:87,032,463A/Glikely benign
rs7488427537:87,032,476G/Cstop gainedpathogenic
rs7704219807:87,032,487A/Tuncertain significance
rs25467389917:87,032,492A/Glikely benign
rs3703108677:87,032,496G/Aconflicting classifications of pathogenicity
rs14313824967:87,032,499G/Alikely benign
rs18079295117:87,032,502T/Clikely benign
rs15629464327:87,032,507G/Tuncertain significance
rs7666722657:87,032,519G/Cuncertain significance
rs14606305697:87,032,525G/Cuncertain significance
rs81878117:87,032,531T/Cuncertain significance
rs9136212367:87,032,540T/Auncertain significance
rs1405928117:87,032,541C/Tconflicting classifications of pathogenicity
rs25467391987:87,032,543G/Apathogenic
rs15846654007:87,032,549G/Alikely pathogenic
rs8860436507:87,032,551C/Auncertain significance
rs7652962607:87,032,563T/Auncertain significance
rs18079363037:87,032,564G/Apathogenic
rs8669840827:87,032,578C/Tlikely pathogenic
rs18079381847:87,032,580C/Tconflicting classifications of pathogenicity
rs25467393487:87,032,587G/Cuncertain significance
rs9050259197:87,032,592A/Cpathogenic
rs15629466597:87,032,596T/Auncertain significance
rs316537:87,032,613A/Gdownstream gene variantbenign
rs7611476387:87,035,591C/Glikely benign
rs7645139987:87,035,603C/Tpathogenic
rs1219184427:87,035,609G/Amissense variantpathogenic
rs25467460337:87,035,612A/Glikely benign
rs3684582957:87,035,613C/Tconflicting classifications of pathogenicity
rs1450564647:87,035,614G/Auncertain significance
rs7525783707:87,035,619G/Aconflicting classifications of pathogenicity
rs1388507867:87,035,639C/Tuncertain significance
rs25467462237:87,035,643T/Clikely benign
rs8860440117:87,035,654T/Guncertain significance
rs15629488817:87,035,656A/Guncertain significance
rs3724274707:87,035,659A/Guncertain significance
rs10355509707:87,035,675C/Auncertain significance
rs7714374317:87,035,679C/Gconflicting classifications of pathogenicity
rs7474535837:87,035,681G/Auncertain significance
rs7691585767:87,035,682G/Alikely benign
rs3713944877:87,035,688G/Aconflicting classifications of pathogenicity
rs25467464597:87,035,691T/Clikely benign
rs25467465137:87,035,703A/Glikely benign
rs7664024947:87,035,709G/Aconflicting classifications of pathogenicity
rs25467465417:87,035,715G/Alikely benign
rs8860624597:87,035,718G/Aconflicting classifications of pathogenicity
rs8860441997:87,035,719C/Tuncertain significance
rs8663010897:87,035,723C/Tuncertain significance
rs25467466207:87,035,740T/Cuncertain significance
rs1482798757:87,035,741G/Apathogenic
rs3733384707:87,035,743G/Cuncertain significance
rs18081989897:87,035,748G/Alikely benign
rs12823387737:87,035,753C/Tuncertain significance
rs7569827517:87,035,754G/Alikely benign
rs8860447067:87,035,756G/Cuncertain significance
rs7579312037:87,035,764C/Tconflicting classifications of pathogenicity
rs7465074727:87,035,775G/Alikely benign
rs13587796937:87,035,781G/Tlikely benign
rs18082028207:87,035,782A/Cuncertain significance
rs14397043667:87,035,791G/Auncertain significance
rs316557:87,035,792C/Tuncertain significance
rs1390428037:87,035,794T/Cconflicting classifications of pathogenicity

Showing 100 of 792 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.