DOT1L

DOT1 like histone lysine methyltransferase

Summary

The protein encoded by this gene is a histone methyltransferase that methylates lysine-79 of histone H3. It is inactive against free core histones, but shows significant histone methyltransferase activity against nucleosomes. [provided by RefSeq, Aug 2011]

Known Variants119 total

rsidPosition (GRCh37)AllelesClassClinVar
rs36766146319:2,164,273C/Gbenign
rs480720519:2,167,878A/Gupstream gene variant
rs1298335719:2,170,868G/A
rs1298641319:2,170,954A/G
rs1297817919:2,172,378T/Cintron variant
rs811294819:2,175,005T/G
rs1066942119:2,175,007T/A
rs1188099219:2,176,403G/Aintron variant
rs1245935019:2,176,586A/Gregulatory region variant
rs1298274419:2,177,193C/Gintron variant
rs224012819:2,187,276T/Cintron variant
rs1260845519:2,187,793T/Cregulatory region variant
rs15031632519:2,189,749G/Abenign
rs202270896619:2,189,785C/Guncertain significance
rs214474241919:2,191,146G/Auncertain significance
rs75954592319:2,191,154C/Tlikely benign
rs1187905419:2,191,211C/Tbenign
rs18901390519:2,193,788C/Tbenign
rs76883269619:2,194,523C/Tuncertain significance
rs226987919:2,194,896T/Cintron variant
rs1298354619:2,195,065G/Tintron variant
rs226988119:2,195,799A/Gintron variant
rs76238735819:2,199,917G/Auncertain significance
rs20144185419:2,206,738C/Tlikely benign
rs214481531119:2,207,672G/Auncertain significance
rs146695097619:2,210,486G/Auncertain significance
rs140010461819:2,210,489G/Aconflicting classifications of pathogenicity
rs14212701019:2,210,497C/Tbenign
rs74569124019:2,210,687G/Auncertain significance
rs7637579019:2,210,736C/Tlikely benign
rs37116220019:2,210,795C/Tuncertain significance
rs20000453119:2,210,815G/Auncertain significance
rs74589101519:2,211,141G/Alikely benign
rs52899817919:2,211,175G/Auncertain significance
rs20192942419:2,211,179C/Tuncertain significance
rs127196045319:2,213,599A/Cuncertain significance
rs74754538919:2,213,614G/Auncertain significance
rs77270153319:2,213,621T/Guncertain significance
rs202379108019:2,213,631T/Guncertain significance
rs251241119819:2,213,878C/Auncertain significance
rs37603247519:2,213,968G/Alikely benign
rs214485235619:2,213,980C/Tuncertain significance
rs11603315619:2,214,484C/Tlikely benign
rs37027676319:2,216,358G/Alikely benign
rs251242092019:2,216,477G/Cuncertain significance
rs37225831719:2,216,482C/Auncertain significance
rs75422703719:2,216,539G/Auncertain significance
rs136815174919:2,216,604T/Cuncertain significance
rs76388642319:2,216,616C/Tuncertain significance
rs55798325919:2,216,619G/Auncertain significance
rs37444896319:2,216,625C/Tuncertain significance
rs77689825919:2,216,629C/Tuncertain significance
rs55498836019:2,216,630G/Alikely benign
rs76993796419:2,216,631C/Tuncertain significance
rs37044954519:2,216,722A/Guncertain significance
rs128505738919:2,216,740C/Tuncertain significance
rs251242590519:2,216,962A/Guncertain significance
rs56209924119:2,217,014G/Tlikely benign
rs77344890119:2,217,767G/Auncertain significance
rs20184357619:2,217,786G/Alikely benign
rs75771148219:2,217,790A/Tuncertain significance
rs54474960519:2,217,905C/Tlikely benign
rs214487843319:2,217,918G/Auncertain significance
rs36774538319:2,220,152A/Tuncertain significance
rs134287716119:2,222,059C/Auncertain significance
rs101327050119:2,222,110G/Auncertain significance
rs76054257419:2,222,151C/Tuncertain significance
rs20001394119:2,222,158C/Tuncertain significance
rs92318358919:2,222,175G/Cuncertain significance
rs104357041019:2,222,202C/Guncertain significance
rs57137521419:2,222,232G/Auncertain significance
rs75319366519:2,222,242A/Guncertain significance
rs76980020019:2,222,284G/Tuncertain significance
rs14416541919:2,222,325G/Alikely benign
rs214490503319:2,222,360C/Guncertain significance
rs20164604919:2,222,372C/Tbenign
rs20187202819:2,222,379G/Auncertain significance
rs76906157519:2,222,430C/Tuncertain significance
rs76733358019:2,222,457C/Tuncertain significance
rs156836788119:2,222,458C/Auncertain significance
rs3496461819:2,222,471A/Tbenign
rs11558545819:2,223,282C/Tbenign
rs202420487919:2,223,406A/Tuncertain significance
rs37696188819:2,223,416A/Guncertain significance
rs121777994119:2,223,425A/Guncertain significance
rs214491313919:2,223,448G/Auncertain significance
rs139983208419:2,225,434C/Tuncertain significance
rs101661064619:2,226,185G/Tuncertain significance
rs78106069819:2,226,209C/Tuncertain significance
rs74629629919:2,226,230A/Glikely benign
rs92752544119:2,226,268G/Cuncertain significance
rs94908085519:2,226,287C/Tuncertain significance
rs37648766719:2,226,316G/Alikely benign
rs20025187619:2,226,415T/Cuncertain significance
rs75173685719:2,226,416C/Tuncertain significance
rs54004454819:2,226,428C/Guncertain significance
rs77301994319:2,226,443C/Guncertain significance
rs95163624219:2,226,556G/Auncertain significance
rs139011495319:2,226,610G/Cuncertain significance
rs74563811819:2,226,649G/Tuncertain significance

Showing 100 of 119 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.