HLA-DRB5

major histocompatibility complex, class II, DR beta 5

Summary

HLA-DRB5 belongs to the HLA class II beta chain paralogues. This class II molecule is a heterodimer consisting of an alpha (DRA) and a beta (DRB) chain, both anchored in the membrane. It plays a central role in the immune system by presenting peptides derived from extracellular proteins. Class II molecules are expressed in antigen presenting cells. The beta chain is approximately 26-28 kDa and its gene contains 6 exons. Exon one encodes the leader peptide, exons 2 and 3 encode the two extracellular domains, exon 4 encodes the transmembrane domain and exon 5 encodes the cytoplasmic tail. Within the DR molecule the beta chain contains all the polymorphisms specifying the peptide binding specificities. Typing for these polymorphisms is routinely done for bone marrow and kidney transplantation. There are multiple pseudogenes of this gene. [provided by RefSeq, Feb 2020]

Known Variants66 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1156414446:32,485,062C/Gdownstream gene variant
rs1127495946:32,485,397G/A3 prime UTR variant
rs1510028026:32,485,410G/C
rs1146042226:32,485,623A/Gintron variant
rs1999109976:32,485,655A/G
rs5594510136:32,485,704T/G
rs2016999456:32,485,856T/Cbenign
rs2005915866:32,485,857G/Abenign
rs1395476296:32,485,944T/Gintron variant
rs5622416146:32,486,196A/T
rs5620072146:32,486,267T/C
rs5437837956:32,486,276C/T
rs5385696716:32,486,310A/T
rs1996822246:32,486,364G/Csynonymous variant
rs1476690226:32,486,442T/Amissense variant
rs5440688446:32,486,543G/A
rs1167089526:32,486,590T/G
rs5705684366:32,486,877C/A
rs1929559576:32,486,965C/A
rs725084296:32,487,068T/G
rs1428041686:32,487,361G/Asynonymous variant
rs2020544006:32,487,397C/Tlikely benign
rs7712064656:32,487,418C/Tlikely benign
rs24808991856:32,487,421A/Glikely benign
rs1150016266:32,487,462G/Tintron variant
rs1890491846:32,487,474G/Aintron variant
rs5438385406:32,487,494T/G
rs1932767486:32,488,013T/Gintron variant
rs1133972826:32,488,050T/Cintron variant
rs1910186066:32,488,081T/A
rs1148757756:32,489,032A/Tintron variant
rs1126687376:32,489,345A/T
rs1912693366:32,489,596A/Tintron variant
rs7774133256:32,489,716G/Alikely benign
rs7079566:32,489,856C/Tbenign
rs1474404976:32,489,888A/Gmissense variant
rs1154886956:32,490,036C/Tintron variant
rs5500625356:32,490,073A/G
rs5324612686:32,490,218C/T
rs1513200686:32,490,243C/Tintron variant
rs1845384856:32,490,366A/Cintron variant
rs1490790646:32,490,391A/Tintron variant
rs5415058566:32,490,394C/T
rs1408495646:32,490,607A/Gintron variant
rs5661439516:32,490,902A/G
rs1138548816:32,491,732A/G
rs5585340396:32,492,325C/G
rs1122090316:32,492,407T/G
rs1918437816:32,492,967T/G
rs1125878216:32,493,589T/G
rs5415424516:32,493,738C/A
rs1134964646:32,494,011A/C
rs1896004726:32,494,097T/A
rs5632053446:32,494,984A/T
rs725084576:32,496,171C/A
rs5330157776:32,496,481C/T
rs3742489936:32,496,534G/C
rs674499616:32,497,550G/A
rs1173172826:32,497,719A/G
rs715492206:32,497,917C/Amissense variant
rs13774601756:32,497,947G/Alikely benign
rs7650987736:32,497,993A/Glikely benign
rs1484515806:32,498,626G/Aupstream gene variant
rs5501270746:32,499,466G/A
rs768469046:32,499,917C/Tupstream gene variant
rs1863258826:32,499,990G/Aupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.