HSD17B13

hydroxysteroid 17-beta dehydrogenase 13

Summary

Predicted to enable oxidoreductase activity, acting on the CH-OH group of donors, NAD or NADP as acceptor and steroid dehydrogenase activity. Acts upstream of or within positive regulation of lipid biosynthetic process. Located in lipid droplet. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants25 total

rsidPosition (GRCh37)AllelesClassClinVar
rs284561444:88,224,497G/Adownstream gene variant
rs131065404:88,225,318G/Tupstream gene variant
rs1502947964:88,226,399C/Tuncertain significance
rs7555510174:88,226,426G/Auncertain significance
rs1142874734:88,226,437G/Abenign
rs104339374:88,230,100T/Gintron variant
rs1112974714:88,230,501A/Cintron variant
rs104338794:88,231,140G/Cintron variant
rs17345007104:88,231,399G/Tlikely benign
rs13039475814:88,231,416T/Cuncertain significance
rs769266924:88,231,428G/Tbenign
rs623057234:88,231,429G/Amissense variantbenign
rs1114033914:88,231,491G/Abenign
rs10487486384:88,234,987T/Cuncertain significance
rs12308587614:88,235,077C/Tuncertain significance
rs24760064574:88,236,654A/Tuncertain significance
rs7538117184:88,236,670C/Tuncertain significance
rs1389329584:88,236,701G/Abenign
rs2016894244:88,236,759A/Cbenign
rs13405455674:88,238,333C/Tuncertain significance
rs5708096464:88,239,488A/Guncertain significance
rs2005282994:88,243,816G/Cuncertain significance
rs12841079824:88,243,867C/Tuncertain significance
rs24760193574:88,243,924T/Cuncertain significance
rs2008472774:88,243,948A/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.