HTRA1

HtrA serine peptidase 1

Summary

This gene encodes a member of the trypsin family of serine proteases. This protein is a secreted enzyme that is proposed to regulate the availability of insulin-like growth factors (IGFs) by cleaving IGF-binding proteins. It has also been suggested to be a regulator of cell growth. Variations in the promoter region of this gene are the cause of susceptibility to age-related macular degeneration type 7. [provided by RefSeq, Jul 2008]

Known Variants252 total

rsidPosition (GRCh37)AllelesClassClinVar
rs379391710:124,219,275C/Gregulatory region variant
rs1120063810:124,220,544G/Aregulatory region variantrisk factor
rs267259810:124,220,682T/A
rs133184976410:124,221,176T/Auncertain significance
rs249757511610:124,221,177C/Alikely benign
rs132572595510:124,221,178C/Tuncertain significance
rs76100851310:124,221,180G/Tconflicting classifications of pathogenicity
rs90023309810:124,221,183C/Glikely benign
rs75511945710:124,221,188C/Guncertain significance
rs131288644410:124,221,195C/Glikely benign
rs99648318910:124,221,202C/Tconflicting classifications of pathogenicity
rs74559796610:124,221,230C/Tuncertain significance
rs101584485010:124,221,238C/Tlikely benign
rs128783232910:124,221,241T/Cuncertain significance
rs135412262110:124,221,242C/Tuncertain significance
rs122133514810:124,221,244C/Tuncertain significance
rs123281816710:124,221,252C/Alikely benign
rs138135797410:124,221,260C/Tuncertain significance
rs77950428210:124,221,264T/Glikely benign
rs104933110:124,221,270C/Tsynonymous variantlikely benign
rs229387010:124,221,276G/Tsynonymous variantlikely benign
rs209748140810:124,221,280C/Guncertain significance
rs98186801610:124,221,286C/Guncertain significance
rs209748143210:124,221,292G/Auncertain significance
rs58777644810:124,221,294pathogenic
rs213390505810:124,221,294G/Alikely benign
rs143553163110:124,221,295C/Tuncertain significance
rs147321990010:124,221,301C/Tuncertain significance
rs139447251610:124,221,306C/Auncertain significance
rs56516263710:124,221,312G/Tlikely benign
rs145165663110:124,221,316C/Guncertain significance
rs98872405310:124,221,318G/Alikely benign
rs209748147410:124,221,320A/Guncertain significance
rs1153814110:124,221,329A/Cuncertain significance
rs94724770110:124,221,333C/Alikely benign
rs124611425210:124,221,344G/Cconflicting classifications of pathogenicity
rs125928560110:124,221,348C/Tlikely benign
rs92169258310:124,221,355G/Tuncertain significance
rs209748153610:124,221,373G/Cuncertain significance
rs209748155410:124,221,403C/Tlikely pathogenic
rs54120401010:124,221,413C/Guncertain significance
rs147884544310:124,221,414G/Clikely benign
rs249757633710:124,221,428T/Guncertain significance
rs140416325010:124,221,431A/Tuncertain significance
rs155494830210:124,221,435C/Apathogenic
rs213390527610:124,221,451G/Tuncertain significance
rs136886060310:124,221,468G/Alikely benign
rs119451345210:124,221,491G/Tuncertain significance
rs249757661610:124,221,495C/Glikely benign
rs14008874510:124,221,505G/Tbenign
rs137923291910:124,221,506C/Tuncertain significance
rs76534440310:124,221,519G/Tlikely benign
rs155494831810:124,221,527G/Alikely pathogenic
rs213390542110:124,221,538A/Guncertain significance
rs75723754510:124,221,553C/Tuncertain significance
rs121767890210:124,221,566G/Auncertain significance
rs213390546110:124,221,568G/Auncertain significance
rs53008785010:124,221,583T/Gconflicting classifications of pathogenicity
rs75592598510:124,221,585C/Glikely benign
rs77998032010:124,221,598C/Tuncertain significance
rs95238551710:124,221,602C/Auncertain significance
rs100514235210:124,221,605C/Guncertain significance
rs75464548710:124,221,619C/Amissense variantuncertain significance
rs159102211810:124,221,633C/Tlikely benign
rs77263735510:124,221,634G/Cuncertain significance
rs90759785110:124,221,638A/Guncertain significance
rs159102214810:124,221,642T/Clikely pathogenic
rs55003996810:124,221,646C/Aconflicting classifications of pathogenicity
rs228466510:124,226,630G/Anot provided
rs93227510:124,231,464G/Aregulatory region variant
rs8023257810:124,232,915C/Aintron variant
rs7904314710:124,233,181C/Tintron variant
rs7283445310:124,235,226T/Gintron variant
rs1226714210:124,248,242C/Gbenign
rs100368537810:124,248,405C/Alikely benign
rs11487712210:124,248,410G/Tbenign
rs213343831810:124,248,436G/Auncertain significance
rs209749439010:124,248,441C/Tpathogenic
rs86462278110:124,248,442G/Tmissense variantpathogenic
rs3508921210:124,248,449A/Glikely benign
rs78156377710:124,248,462G/Cmissense variantpathogenic
rs37075149610:124,248,463C/Tuncertain significance
rs76866556510:124,248,468G/Auncertain significance
rs155495065510:124,248,481T/Alikely pathogenic
rs249762165610:124,248,484C/Tuncertain significance
rs99376056610:124,248,485C/Tlikely benign
rs147785551410:124,248,492G/Alikely pathogenic
rs76511266810:124,248,514G/Auncertain significance
rs75777842910:124,248,529C/Tlikely benign
rs375084410:124,248,537T/Cbenign
rs77926185010:124,248,930G/Aconflicting classifications of pathogenicity
rs74836789510:124,248,943C/Tuncertain significance
rs77232774610:124,248,944G/Alikely benign
rs143822350210:124,248,954C/Tconflicting classifications of pathogenicity
rs118083523710:124,248,955G/Auncertain significance
rs77339618610:124,248,964C/Tuncertain significance
rs20187882610:124,248,968G/Alikely benign
rs249762275010:124,248,975G/Auncertain significance
rs155495070310:124,248,979C/Gpathogenic
rs136937938810:124,248,981G/Auncertain significance

Showing 100 of 252 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.