L3MBTL3

L3MBTL histone methyl-lysine binding protein 3

Summary

This gene encodes a member of the malignant brain tumor (MBT) family of chromatin interacting transcriptional repressors. Members of this family function as methyl-lysine readers, which recognize methylated lysine residues on histone protein tails, and are associated with the repression of gene expression. The encoded protein may regulate hematopoiesis. Homozygous deletion of this gene has been observed in human patients with medulloblastoma. [provided by RefSeq, Oct 2016]

Known Variants79 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1138980036:130,341,235T/A
rs5472111576:130,341,903G/C
rs77525996:130,343,365A/Gsplice region variant
rs1431261706:130,344,246T/Gintron variant
rs9532616:130,345,699T/Gintron variant
rs14157006:130,345,791G/Aintron variant
rs14157016:130,345,835G/Aintron variant
rs751917386:130,348,257C/G
rs65696486:130,349,119C/A
rs1397195526:130,354,973T/Cintron variant
rs68999766:130,358,428G/Aregulatory region variant
rs7760702326:130,363,870G/Cuncertain significance
rs48958646:130,364,482C/Tintron variant
rs48958656:130,364,491A/G
rs93989346:130,365,016A/Gintron variant
rs45949676:130,366,161A/T
rs77448306:130,367,725T/C
rs77465896:130,371,840G/C
rs7642661496:130,372,516T/Guncertain significance
rs17810818686:130,372,523G/Auncertain significance
rs77568706:130,373,648C/T
rs3756432356:130,374,039A/Guncertain significance
rs7595055766:130,374,066G/Auncertain significance
rs93887686:130,374,102A/Cbenign
rs3776795556:130,374,127T/Guncertain significance
rs43512836:130,374,711T/Cintron variant
rs44256136:130,374,792C/A
rs69004736:130,375,810A/C
rs69238196:130,376,095T/G
rs3676052916:130,376,306C/Alikely benign
rs7680082186:130,376,323A/Guncertain significance
rs2005267296:130,376,350C/Tuncertain significance
rs7761611556:130,376,379G/Tuncertain significance
rs3688398906:130,376,383C/Tuncertain significance
rs7729189116:130,376,399G/Tuncertain significance
rs117590186:130,377,843C/Tintron variant
rs3749850696:130,378,601G/Auncertain significance
rs7646574816:130,378,611C/Tuncertain significance
rs1997345156:130,378,623C/Tuncertain significance
rs14756869546:130,378,637A/Cuncertain significance
rs126612326:130,379,160T/Cintron variant
rs122014926:130,379,282A/Gintron variant
rs77607606:130,379,852A/Gintron variant
rs93757006:130,379,854T/Cintron variant
rs7663151776:130,381,238G/Auncertain significance
rs77672846:130,381,261G/Abenign
rs93757036:130,386,971T/Gregulatory region variant
rs7812508016:130,387,547A/Guncertain significance
rs7659249756:130,387,568A/Guncertain significance
rs3697049816:130,387,609G/Auncertain significance
rs9526170186:130,389,486G/Cuncertain significance
rs785837906:130,389,569A/Gbenign
rs43645066:130,389,940G/Aintron variant
rs104991726:130,390,657G/Cintron variant
rs3745814616:130,392,134C/Tuncertain significance
rs7457055856:130,392,190A/Guncertain significance
rs48973646:130,394,666C/Gintron variant
rs121907246:130,395,960C/Gintron variant
rs132098906:130,396,545T/Gintron variant
rs77567336:130,398,013T/G
rs2002592906:130,399,711C/Tuncertain significance
rs14905128576:130,399,755A/Guncertain significance
rs94924476:130,403,515G/A
rs25354573796:130,404,809G/Auncertain significance
rs25354861326:130,407,288C/Tuncertain significance
rs7641298326:130,407,306A/Guncertain significance
rs9523370816:130,407,312A/Guncertain significance
rs9854075566:130,407,324G/Auncertain significance
rs3744564026:130,407,345A/Glikely benign
rs3863523236:130,413,896T/Cuncertain significance
rs7545955546:130,413,918A/Guncertain significance
rs25355522826:130,413,978C/Tuncertain significance
rs132116836:130,417,833G/T
rs7735346656:130,425,614C/Tuncertain significance
rs7633754166:130,425,615G/Auncertain significance
rs1419900196:130,442,067A/Cuncertain significance
rs7695440826:130,454,687G/Auncertain significance
rs7494158226:130,454,722G/Tuncertain significance
rs25359827656:130,460,798T/Cuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.