LACC1

laccase domain containing 1

Summary

This gene encodes an oxidoreductase that promotes fatty-acid oxidation, with concomitant inflammasome activation, mitochondrial and NADPH-oxidase-dependent reactive oxygen species production, and bactericidal activity of macrophages. The encoded protein forms a complex with fatty acid synthase on peroxisomes and is thought to be modulated by peroxisome proliferator-activated receptor signaling events. Naturally occurring mutations in this gene are associated with inflammatory bowel disease, Behcet's disease, leprosy, ulcerative colitis, early-onset Crohn's disease, and systemic juvenile idiopathic arthritis. [provided by RefSeq, Apr 2017]

Known Variants31 total

rsidPosition (GRCh37)AllelesClassClinVar
rs159488293313:44,455,124G/Apathogenic
rs3441439613:44,455,233A/Glikely benign
rs76015706913:44,455,234A/Guncertain significance
rs195500334413:44,455,240A/Cuncertain significance
rs254759918113:44,455,293C/Auncertain significance
rs14134766313:44,455,296G/Cuncertain significance
rs76038576813:44,455,335C/Auncertain significance
rs77775387413:44,455,374G/Auncertain significance
rs137627297613:44,455,443C/Glikely benign
rs75899496613:44,455,480A/Guncertain significance
rs19958010513:44,455,544G/Alikely benign
rs15020270013:44,455,558C/Guncertain significance
rs254760068713:44,455,603A/Cuncertain significance
rs77512623013:44,455,612T/Guncertain significance
rs13870171713:44,455,624T/Cuncertain significance
rs254760080013:44,455,626A/Guncertain significance
rs254760105713:44,455,672C/Guncertain significance
rs13827870613:44,456,447G/Auncertain significance
rs195510808413:44,456,449A/Guncertain significance
rs14295821913:44,456,492G/Auncertain significance
rs376414713:44,457,925A/Gmissense variantbenign
rs120274192813:44,457,936G/Cuncertain significance
rs254760892413:44,457,946G/Auncertain significance
rs75821694113:44,457,960T/Clikely benign
rs77437605213:44,457,997G/Cuncertain significance
rs73088029513:44,458,015T/Cmissense variantpathogenic
rs7973409913:44,463,003C/Tbenign
rs52935447513:44,464,263C/Auncertain significance
rs18437080913:44,464,356C/Tpathogenic
rs254762447213:44,464,398A/Guncertain significance
rs1050752213:44,479,000G/Auncertain risk allele

Gene information from NCBI Gene. Variant classifications from ClinVar.