NR1H3

nuclear receptor subfamily 1 group H member 3

Summary

The protein encoded by this gene belongs to the NR1 subfamily of the nuclear receptor superfamily. The NR1 family members are key regulators of macrophage function, controlling transcriptional programs involved in lipid homeostasis and inflammation. This protein is highly expressed in visceral organs, including liver, kidney and intestine. It forms a heterodimer with retinoid X receptor (RXR), and regulates expression of target genes containing retinoid response elements. Studies in mice lacking this gene suggest that it may play an important role in the regulation of cholesterol homeostasis. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Oct 2011]

Known Variants35 total

rsidPosition (GRCh37)AllelesClassClinVar
rs375866911:47,272,579A/T
rs1083868111:47,275,064G/C
rs432091711:47,277,094T/Cregulatory region variant
rs375867211:47,278,417A/Gupstream gene variant
rs375867311:47,278,917C/G
rs1222149711:47,280,653G/A5 prime UTR variant
rs20055784611:47,280,724C/Aregulatory region variant
rs1103915511:47,280,762G/Aregulatory region variant
rs76952620611:47,280,804C/Tlikely benign
rs13943852511:47,281,365C/Auncertain significance
rs98715539711:47,281,377G/Cuncertain significance
rs75025622511:47,281,384G/Auncertain significance
rs4148144511:47,281,453G/Tbenign
rs76089461811:47,281,978G/Auncertain significance
rs227923811:47,282,024C/Tsynonymous variant
rs3497417611:47,282,060T/Clikely benign
rs76187381711:47,282,103G/Auncertain significance
rs78095988711:47,282,120C/Tlikely benign
rs75204608111:47,282,202C/Tuncertain significance
rs76378272511:47,282,847A/Tuncertain significance
rs14792280111:47,282,867T/Cuncertain significance
rs254057722811:47,282,869C/Tuncertain significance
rs77860045811:47,283,128C/Tuncertain significance
rs20048560911:47,283,237G/Auncertain significance
rs143322194411:47,283,255T/Cuncertain significance
rs4127518611:47,283,415A/Gintron variant
rs15019130811:47,283,492G/Auncertain significance
rs52785782911:47,283,515A/Cuncertain significance
rs74649933611:47,283,551G/Auncertain significance
rs1083868411:47,283,862A/T
rs712011811:47,286,290T/G
rs648574611:47,286,666A/Gupstream gene variant
rs254066030511:47,289,490A/Guncertain significance
rs77907715711:47,290,124G/Cuncertain significance
rs77930621411:47,290,201A/Guncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.